Tashin jini na fatar jiki (FTD) wani nau'i ne na rikici wanda ake kira da sunan cutar Pick. Ya ƙunshi ƙungiyar cuta wadda take shafi hali, motsin zuciyarmu, sadarwa da cognition . Wasu sunayen da aka yi amfani da FTD sun hada da:
- ci gaba na gabanotemporal
- frontal jiki dementia
- Pick na hadaddun
- gabanin ƙaurawar lobar degeneration
A FTD, gabanin da na lobes na kwakwalwa suna shafar da kuma inrophy (shrink) a cikin girman.
FTD yawanci yana kama da ƙananan matasa (50s zuwa 60s), amma an gano shi a cikin mutane da shekarun da suka wuce 21 kuma sun tsufa a matsayin marigayi 80s. Kimanin kashi 60% na lokuta na FTD ne mutanen da ke da shekaru 45 zuwa 64.
Arnold Pick da farko ya gano adadin lamarin lamarin da ke cikin kwakwalwa (wanda aka kira jikin Pick) a shekara ta 1892. Jikunan jikin sun kasance a wasu nau'i na FTD kuma ana ganin su ne kawai a karkashin wani microscope a lokacin da ake daukar su.
Irin FTD
Hanyoyi hudu da suka fada cikin cikin FTD sun hada da:
- Ra'ayin Bayani Dangantaka Dangantaka
Kamar yadda sunan yake magana, bambancin hali na FTD yana tasiri hali, haifar da haɗin kai da rashin dacewa . - Farfesa na Farko Aphasia
Babban nau'i na irin wannan FTD shine aphasia , wanda ke nufin rashin lahani a cikin ikon harshe. Wannan na iya rinjayar duka ikon yin sadarwa da fahimta. - Ci gaba na Supranuclear Palsy
Supranuclear palsy yana shafar daidaito da motsi, kazalika da ƙwarewar ƙwarewa. Bambanci alama ce ta ɓacin ido.
- Corticobasal Degeneration
Hanyoyin cututtukan ganyayyaki na corticobasal sau da yawa suna bayyana kamar rauni ne da tsoka, kuma yakan fara ne kawai a gefe guda na jiki. Matsaloli tare da ƙwaƙwalwar ajiya da halayen suna ci gaba kamar yadda ciwon ya ci gaba.
Bayyanar cututtuka na FTD
Mutanen da ke da FTD suna nuna halin halayyar al'umma da ba daidai ba, kamar maganganun da ba shi da hankali, rashin fahimta ko jin dadin zuciya, damuwa, karuwa da sha'awar jima'i, ko manyan canje-canje a cikin abubuwan da ake so.
Sauran suna nuna rashin lafiya, maganganu akai-akai ko al'amuran, rashin ƙarfi da kuma dalili mara kyau. Hakanan suna iya samun tasiri ko mummunan tasiri , ma'anar cewa fuskokinsu ba su nuna kadan ko ba a nuna murmushi ba, ciki har da baƙin ciki, farin ciki, ko fushi.
FTD sau da yawa yana rinjayar damar yin sadarwa a cikin jawabai biyu (ikon yin amfani da kalmomi don bayyana kanka) da kuma jawabin karɓa (ikon fahimtar magana). Kowane mutum na iya zama matsala gano kalmomin da ya dace, yi magana sosai da jinkirin kuma sannu a hankali, yana da wuyar karantawa da rubutu daidai, kuma baza su iya tsara kalmomi a hanyar da ta dace ba.
Canjin Canje-canje
FTD sau da yawa yana rinjayar da ikon sarrafa tsarin motsi da sauran ayyukan motar. Wadanda suke tare da FTD suna iya fadawa akai-akai ko suna da ƙafa maras so da kafa ƙungiyoyi ko shakiness.
Abin sha'awa, ƙwaƙwalwar mutum da kuma fahimtar yanayin da suke kewaye da su sau da yawa yana kasancewa mai ƙaƙƙarfa, musamman ma a farkon matakan.
Yaya FTD da Alzheimer suka Bambanta?
A cikin Alzheimer, ainihin alamar cututtuka sune rashin kuskuren ƙwaƙwalwar ajiya da wahalar samun sabon abu. A cikin FTD, ƙwaƙwalwar ajiya tana kasancewa marar kyau tun farko; bayyanar cututtuka na farko sun haɗa da haɗari tare da hulɗar zamantakewar jama'a da motsin zuciyarmu, kazalika da wasu ƙalubale na harshe.
FTD da Alzheimer sun bambanta yadda kwakwalwar ta shafi jiki. FTD yafi rinjayar layin kwakwalwa da na lobes; yayin da Alzheimer ke kula da tasirin mafi yawancin kwakwalwa.
FTD ma yana ƙaddamar da ƙananan yara. Yawan shekarun farkon FTD kimanin shekara 60 ne. Duk da yake wasu mutane sun fara da Alzheimer, yawancin marasa lafiya sun wuce 65 kuma yawancin wadanda ke cikin shekarunsu 70 ko 80.
Abin da ke haifar da FTD?
Ba a san dalilin FTD ba. Duk da yake mafi yawan lokuta na FTD sun fara samuwa ta hanzari, kwayoyin halitta suna taka muhimmiyar rawa a wasu lokuta. Kusan kashi 10 cikin dari na lokuta za'a iya dawowa zuwa canji a cikin wani nau'i guda.
Wannan maye gurbin jinsi yana da gadon kai tsaye, ma'ana cewa idan mahaifiyarka ko uba yana da wannan takaddama na musamman ga FTD, kana da 50% damar samun bunkasa FTD.
Ƙarin 20% zuwa 40% na mutanen da aka gano tare da FTD suna da haɗin haɗin iyali inda an sami alamun fiye da ɗaya fiye da ɗaya fiye da ɗaya da FTD.
Sanin asali
Hakazalika da bincikar cutar Alzheimer , babu wani gwajin da zai iya gano FTD. Magunguna yawanci suna shan gwajin gwaji irin su MRI ko PET binciken ; gwaji na auna don auna ƙwaƙwalwar ajiya da kuma iyawar halayen harshe; gwajin motsi jiki; watakila wani famfo na asali ; da kuma wasu gwaje-gwaje na jini. An gano asali ta tattara duk sakamakon daga waɗannan gwaje-gwaje, yana yanke hukunci akan wasu ƙananan kamfanoni irin su bitamin B12 ko cututtuka, da kwatanta alamar cututtuka ga wasu lokuta na FTD. Yana da mahimmanci cewa likitan ne wanda ke da masaniya da FTD da sauran nau'in nakasa na shiga cikin wannan kimantawa tun lokacin da wasu fannoni na FTD suka shafi sauran cututtuka.
Jiyya
Babu magani wanda ke kai ga irin wannan lalata, don haka manufar kulawa ita ce ta sarrafa magunguna kamar yadda ya yiwu. Magungunan likita zasu iya rubuta magungunan da ake amfani dasu don matsalolin motsi a cutar cutar Parkinson , ciki har da Carbidopa / levodopa (Sinemet) . Wani lokaci ana yin maganin FTD tare da magungunan antipsychotic idan magungunan miyagun ƙwayoyi ba su da tasiri.
Magungunan maganin antidepressant, musamman masu zaɓin masu kwantar da hankali na serotonin (SSRIs), sun nuna wasu amfana a zalunta wasu matsalolin da ke damun FTD. Wasu likitoci za su kuma rubuta magungunan da aka ba wa marasa lafiya na Alzheimer, ciki har da masu haɓakawa na cholinesterase . Bincike, duk da haka, bai bayyana wadannan magunguna sosai ba don FTD duk da haka.
Harkokin sana'a da na jiki za su iya amfanar da marasa lafiya ta hanyar taimakawa wajen ragewa da motsi na motar da motsa jiki, yayin da maganganu na iya taimakawa wasu lokuta ta hanyar sadarwa.
Yanayin Yanayi na Fassarar Duka
Kimanin kashi 10% zuwa 20% na duk wani rikici ne FTD, wanda ke fassara zuwa kimanin 50,000 zuwa 60,000 Amirkawa. FTD yana daya daga cikin nau'in nakasar da aka fi yawanta a kananan yara fiye da shekaru 65, kuma ya fi kowa a cikin maza fiye da mata.
Faɗakarwa
Mahimmancin FTD ba shi da kyau. Zuwan rai yana jigilar ko'ina daga cikin shekaru biyu zuwa 20 bayan ganewar asali, dangane da gudun gaba da ci gaba da kuma sauran cututtuka. FTD ba zai haifar da mutuwa ba, amma yana haifar da yaki da wasu cututtuka da cututtuka da wuya.
> Sources:
> Ƙungiyar Ƙungiyar Harkokin Fuskantarwa. Sanin asali.
> Ƙungiyar Ƙungiyar Harkokin Fuskantarwa. Hadin gwiwa na farko.
> Ƙungiyar Ƙungiyar Harkokin Fuskantarwa. Genetics.
> Ƙungiyar Ƙungiyar Harkokin Fuskantarwa. Menene FTD?
> Cibiyar Nazarin Harkokin Kimiyyar Halitta, ta {asa, na {asar Amirka. Binciken Lafiya na Madauki. Cutar da Take.
> Jami'ar California, San Francisco. Forms of Frontotemporal Dementia.
> Jami'ar California, San Francisco. FTD mai zaman kansa.
> Cibiyoyin Kula da Lafiya ta Amirka. Cibiyar Kasa ta Kasa. Iri na Cutar Duka.