Cutin cututtuka: Ƙwararren Yanayi na Farfaɗɗun Bayanin

Irin wannan Maganin Farfaɗar Tsuntsauran Tsakanin Yau Har ila yau Ana Magana da Cututtuka na Pick

Bambancin bambancin launi na frontotemporal (bvFTD) yana daya daga cikin nau'i-nau'i da dama da suka fada cikin "layinin" frontotemporal degeneration ". Wannan rukuni yana rinjayar kusan 50,000 zuwa 60,000 Amirkawa. Kamar yadda sunan ya nuna, wannan nau'i ne na farko yana rinjayar frontal da kuma lobes na kwakwalwa. Maganganun da aka fi sani da su gaba ɗaya shine na nau'i-nau'i-nau'i-nau'i.

Yayin da ake kira ƙwayar cuta ta gaba-gaba-gaba-nau'i-nau'in ƙwayar cuta mai mahimmanci .

Mene ne Yake Cutar da Cutar?

Anyi zaton cutar ta zamo ta lalacewa ta hanyar rikicewar nau'o'in sunadarin proteins a gabanal da na lobes na kwakwalwa. Wadannan fuka-furotin sunadaran suna jikin jiki. Yayinda suke tarawa a cikin wadannan lobes, kwayoyin kwakwalwa sun fara mutuwa, suna haifar da canji, halayyar halayyar juna da kuma haɓaka a cikin aiki.

Cutar cututtuka

Abubuwan da suka fi dacewa na bvFTD sune kalubale na halin mutum , ciki har da matsananciyar cin zarafi, da ciwon halayyar mutum, da yin maganganu marasa dacewa, da kuma nuna jima'i da kuma aiki, tare da rashin tausayi, tashin hankali , rashin tausayi da son kai.

Mutanen da ke da bvFTD suna da matsala wajen aiki da aiki, nuna rashin lafiya a tsabtace su, kullun wasu abubuwa, da zaɓin kuɗi mara kyau, da kuma kusantar dangi da abokai ta hanyar maganganunsu da halayen da ba su da hankali.

Wasu mutane tare da bvFTD kuma suna fuskantar matsalolin motsi kamar cutar ta Parkinson , ciki har da rage girman hangen nesa, tsofaffin ƙwayar jiki, rauni da rigidity.

Ba kamar Alzheimer ba , ƙwaƙwalwar ƙwaƙwalwar ajiya ba ta bunkasa a bvFTD ba, kuma idan hakan ya faru, ba haka ba har sai cutar ita ce matakan baya.

A matsayin mai kulawa, za ka iya lura da wasu matsalolin ƙwaƙwalwar ajiya, kazalika da kalubale tare da tsarawa ko hankali (dangane da aikin gudanarwa ).

A cikin bvFTD mai tsanani, harshe ya shafi, yin sadarwa mai wuya.

Ta Yaya Cututtukan Mutuwar Bam ya bambanta daga Alzheimer's?

Bambancin bambance-bambance da ke dauke da cutar ta hanyar cutar Alzheimer tun da yake duka cututtuka sun shafi rinjaye, halayyar da halayen su. A baya lokuttan bayyanar cutar cutar, sune gaba ɗaya da canje-canje a cikin tausayi, hukunci , gudanarwa da hali, yayin a cututtukan Alzheimer, ƙwaƙwalwar ajiya, daidaitawa da kuma labarun sadarwa sunfi yawa a farkon.

Sanin asali

Binciken na BvFTD sau da yawa ana jinkirtawa tun da farko za'a iya tunanin cewa mutumin da ya shafi mutum yana kasancewa da lalacewa, sonkai, tawayar ko yin aiki. Yayin da ci gaba da alamun bayyanar, duk da haka, iyalai sukan nemi taimakon likitan don ganewar asali da magani. Binciken ganewa ya dogara ne akan kasancewa da alamun bayyanar cututtukan da aka bayyana a sama, da kuma ikon yin sarauta akan wasu rikice-rikice irin su Alzheimer ko na jini . Yin nazarin ka'idodin tsari na bambancin hali na FTD zai iya taimakawa ga iyalan gidan idan BDFTD ke bincikar ko ana daukar shi ta likita.

MRI na iya taimakawa wajen bincikar bvFTD saboda zai nuna wasu atrophy (shrinkage) na kwakwalwar kwakwalwa ta gaba. Yayin da cutar ta ci gaba, atrophy zai kara da yadawa zuwa yankunan da ke cikin gida, da kuma ganglia basal.

Fassara da Rayuwa na Rayuwa (Hasashen Tsare-Tsaren)

Matsayin rai na rayuwa daga farawar bayyanar cututtuka yana da kimanin shekaru takwas zuwa tara, ko da yake wasu mutane na iya rayuwa shekaru 20 ko haka tare da cutar. Kamar yadda yake tare da kowace cuta, zai iya kasancewa wata ƙalubale ga masu kulawa, da kuma wadanda suke fuskantar wannan.

Jiyya

Jiyya na iya kunshi ƙoƙari na yin amfani da hanyoyin dabarun ƙwayoyi ba tare da maganin miyagun ƙwayoyi ba don hana halayen halayen.

Wasu likitoci sun rubuta takardun antidepressants da ake kira masu zanga-zangar sigotin gyaran maganin serotonin (SSRIs), wanda zai iya taimakawa tare da wasu abubuwa masu rikitarwa irin su hoarding ko juyayi.

Kalma daga

Ya zama al'ada don jin damu a wasu lokuta yayin da kuke fuskantar kalubale na bambancin layi na gaba-gaba. Kuna watsi da jaraba don gwada yin hakan da kanka; maimakon haka, nemi taimako ga waɗanda ke kewaye da ku, ko ta hanyar shirin tallafi na al'umma, tattaunawa ta kan layi game da BvFTD ko aboki wanda ke shirye ya fitar da ku don kofi ko zauna a gida tare da ƙaunataccen ku yayin da kuka yi jinkiri.

Bugu da ƙari, Ƙungiyar Ƙungiyar Dattijai ta Fassara ta ƙunshi sunayen ƙungiyoyi na gida da kuma albarkatun kan layi da kuma waya don taimako.

Sources:

Annals of Neurology. Cin da hypothalamus canje-canje a cikin layi na gaba-gaba-bambancen hali. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3084499

Ƙungiyar Ƙungiyar Dattijai. Sakamakon yarjejeniya ta duniya game da bambancin hali na FTD. http://www.theaftd.org/wp-content/uploads/2009/02/Table-3-International-consensus-criteria-for-behavioural-variant-FTD.pdf

Banks, S., Weintraub, S. Journal of Geriatric Psychiatry and Neurology. Ƙwararren cututtuka na Neuropsychiatric a cikin Maɗaukaki Bayani na Farfesa da Farfesa na Farko na Afhasia .. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2892801/

Ma'anar ilimin halitta. Sensitivity of current criteria for the diagnosis of behavioral variant frontotemporal dementia. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2821829/

Jami'ar California, San Francisco. Ci gaba na ciwo: FTD mai bambancin ra'ayi. http://memory.ucsf.edu/ftd/overview/ftd/progression/multiple