Cutar cututtuka, ganewar asali da jiyya na Pheochromocytoma
A pheochromocytoma ne irin ciwon da aka samu a cikin adrenal gland ko wasu jijiya Kwayoyin. Wadannan ciwace-ciwacen suna da wuya amma suna iya haifar da bayyanar cututtuka domin suna yaduwa da yawa daga wasu kwayoyin hormones da ake kira catecholamines . Ko da yake wasu pheochromocytomas zasu iya tasowa a cikin kwayoyin jikinsu, kusan dukkanin su suna samuwa a cikin daya daga cikin glanders.
Wadannan ciwace-ciwacen sun kasance kusan ma wadanda basu iya cin nasara ba, amma har yanzu suna buƙatar magani saboda halayen halayen hormone.
Facts Game da Pheochromocytoma da Ruwan jini
- Pheochromocytomas suna samar da matakan sunadarai da ake kira catecholamines, waxanda suke da hawan haɗari masu haɗari da haɗari, kuma suna aiki a kan tsarin zuciya don kara yawan zuciya, karfin jini, da jini.
- Wadannan ciwace-ciwacen suna samar da epinephrine (adrenaline), norepinephrine da dopamine - mahadi uku waɗanda suke cikin mafi karfi da aka sani don kara karfin jini . Jiki yana amfani da ƙananan yawa daga cikin wadannan sunadarai don magance matsalolin haɗari ko damuwa.
- Koda a cikin ƙananan kuɗi, duk uku suna da babban illa a kan karfin jini.
- Saboda pheochromocytomas suna samar da yawancin waɗannan kwayoyin halittar, wadannan tasirin da ke kan cutar karfin jini suna da ban mamaki sosai.
- Kusan dukkan marasa lafiya tare da pheochromocytomas sun karu da hawan jini, kuma alamar cutar hawan jini da wannan lalacewar ta haifar shi ne saurin hawan jini a yayin rana.
Alamun & cututtuka na Pheochromocytoma
A classic kungiyar na bayyanar cututtuka a lokuta na pheochromocytoma ake kira a matsayin "triad" kuma kunshi:
- Ciwon kai
- Sugar wucewa
- Tachycardia
Tsawan jini mai karfin gaske, yawanci mafi girma, shi ne mafi yawan alamu a cikin marasa lafiya tare da pheochromocytoma. Sauran, ƙananan alamun cututtuka sun haɗa da:
- Matsalar Kayayyakin (hangen nesa)
- Asarar nauyi
- Ƙishirwa da yawa / urination
- Babban jini sugar
Duk waɗannan bayyanar cututtuka na iya haifar da cututtuka daban-daban, don haka yana da muhimmanci a likita ta likita.
Pheochromocytoma ganewar asali
Yawancin pheochromocytomas an gano su ne ba zato ba tsammani ("ta hanyar hadari") a lokacin wani nau'i na binciken hotunan (MRI, CT Scan) da aka yi don matsala maras dangantaka. Tumors da aka gano a wannan hanya yawanci suna kama da ƙananan juji ko taro dake a yankin kusa da kodan. Tarihin iyali ko wasu nau'ikan bayanan alamun alaƙa zasu iya nuna wa likita cewa mai yiwuwa pheochromocytoma ya kasance.
Wadannan ciwace-ciwacen suna da nasaba da wasu, irin yanayin yanayi. Sanin ganewa yawanci yakan hada da aunawa matakan hormone da yawa a kan ɗan gajeren lokaci (24 hours ne na hali), kazalika da ɗaukan hotuna na dukan kirji da ciki. Wani lokaci ana gwagwarmaya gwajin gwagwarmaya, inda likita zai buge abu ɗaya, jira ɗan gajeren lokaci, sa'annan zana zub da jini kuma duba don gano idan abu mai ƙwayar ya kara yawan adadin sauran kwayoyin jini.
Pheochromocytoma Jiyya
Dukkanin pheochromocytomas da ake bukata a cire su a hankali. Duk da yake karfin jini ba shi da mahimmanci a yanke shawarar ko ko dai ba za a yi aikin tiyata ba, wannan yana daya daga cikin lokuta masu wuya inda aka yi ƙoƙari don rage karfin jini kafin a yi aikin tiyata.
Dalilin da ya sa wannan yana da rikitarwa amma ya danganta da gaskiyar cewa wannan haɗari ne mai hadarin gaske kuma mai haɗari.
Don rage girman haɗari, an saita matakan daidaitaccen matakai, ko da yake wasu daga cikin wadannan matakai suna tayar da karfin jini. Tun da yawancin karfin jini ya karu, haɓaka ƙari zai iya zama haɗari. Ainihin tiyata za a yi ta kwararren likita da gwaje-gwaje na musamman a duk lokacin da kuma bayan tiyata don tabbatar da cewa an cire dukan ciwon ciki.
Sources:
Baguet, JP, Hammer, L, Mazzuco, TL, et al. Yanayi na ganowar phaeochromocytoma: nazarin nazari na 41 na marasa lafiya. Turai Journal of Endocrinology 2004; 150: 681.
Bravo, EL. Tsarin ra'ayoyinsu a cikin pathophysiology, ganewar asali, da kuma maganin pheochromocytoma. Endocrinology Review 1994; 15: 356.
Oishi, S, Sasaki, M, Ohno, M, et al. Tsakanin hawan jini da gudanarwa a cikin marasa lafiya tare da pheochromocytoma. Ra'ayin rahoton da kuma nazarin wallafe-wallafe. Japan Heart Journal 1988; 29: 389.
Stein, PP, Black, HR. Kyakkyawan tsarin bincike don pheochromocytoma. Binciken wallafe-wallafe da rahoto na dandalin ma'aikata ɗaya. Medicine (Baltimore) 1991; 70:46.
Ulchaker, JC, Goldfarb, DA, Bravo, EL, Novick, AC. Sakamakon nasara a cikin tiyata pheochromocytoma a zamanin zamani. Journal of Urology 1999; 161: 764.