Magungunan ƙwararriya mai tsari (TEN) wani mummunar cututtukan fata ne wanda ke haifar da fatawa a karkashin fata (erythema), mutuwar fata na fata ( necrosis ), da kuma ƙyamar fata da jikin mucous membranes. TEN ba shi da nasaba da kowace kabila ko jinsi. Duk da yake yanayin zai iya haifuwa ta hanyar kamuwa da cuta ko ciwace-ciwacen ƙwayar cuta, yawancin lokuta suna da nasaba da maganin miyagun kwayoyi.
Magunguna da aka sani don yin TEN
Drugs da aka sani da ya sa TEN sun hada da:
- Kwayoyin rigakafi irin su sulfonamides, penicillins , macrolides, da quinolones
- Anticonvulsant (antiseizure) kwayoyi
- Magungunan anti-inflammatory marasa ciwon steroidal (NSAIDs)
- Allopurinol
- Matsayin necrosis na tumor (TNF) -an kwayoyi irin su Remicade (infliximab), Enbrel (etanercept), da Humira (adalimumab)
Abubuwan da aka yi amfani da miyagun ƙwayoyi yawanci yakan faru a cikin mako guda zuwa uku na farawa da magani. Abu ne mai wuya don maganin miyagun ƙwayoyi ya faru bayan makonni takwas. Kimanin kashi ɗaya cikin uku na shari'o'in suna haifar da abubuwan ban sani ba.
Cutar cututtuka
Maganin ciwon kwari mai laushi kullum yana farawa tare da mura-kamar bayyanar cututtuka irin su zazzabi, tari, ciwon makogwaro, ƙwaƙwalwar hanci, da kuma rashin jin daɗin jiki na kwana biyu zuwa uku. Wadannan bayyanar cututtuka zasu iya cigaba da haɗuwa da:
- Ƙananan raunin ja wanda yayi girma a cikin manyan launi na fata wanda ke rufe kashi 30 ko fiye na jiki
- Cikakken ƙwaƙwalwa da laushi na fata
- Sakamakon m, ja, wuraren zafi inda fata ta filaye
- Tatsatse, launi na zub da jini wanda ke haifar da tsirrai
- Sore idanu ( conjunctivitis )
- Jin zafi
Wadannan bayyanar cututtuka yawanci na takwas zuwa 12. Saboda mummunar wadannan bayyanar cututtuka, matsalolin na iya ci gaba, kamar su ciwon huhu ; raguwa da ƙwayoyin mucous a cikin baki, makogwaro da magunguna; fata cututtuka; gazawar koda , gubawar jini ( sepsis ), da kuma girgiza.
Idan ba tare da magancewa ba, da yawa daga cikin waɗannan lalacewar na iya zama m.
Sanin asali
TEN an samo asali ne bisa ga yawan bayyanar cututtuka da kuma bincikar fata. Sauran cututtukan fata, irin su staphylococcal scalded fata cututtuka, na iya samun irin wannan bayyanar cututtuka. Sau da yawa, za a dauki samfurin fata (biopsy) don tabbatar da TEN kuma ya fitar da duk wani cuta.
Jiyya
Maganin zane-zane mai laushi zai iya haifar da matsalolin rayuwa. Idan kun yi tunanin za ku iya samun TEN, ku nemi magani. Ana la'akari da TEN wani gaggawa na likita kuma yana buƙatar kulawa mai kyau. A baya yanayin da aka bi, mafi mahimmancin ƙwarewar shine. Zaɓuɓɓukan jiyya sun haɗa da:
- Tsayawa duk magunguna wanda zai haifar da TEN
- Rashin ruwa mai zurfi (IV) ruwa da masu amfani da wutar lantarki
- Cirewa daga matattu fata fata (debridement)
- Bandages masu karewa
- Alurar rigakafi don hana ko magance cututtuka
- Pain magani
- Yin maganin matsaloli irin su ciwon huhu ko koda
- Yin amfani da ɗakun abincin da za a ba da kayan abinci
Jiyya na iya hada da immunoglobulin, cyclosporine, plasmapheresis , ko oxygen. Nazarin ya nuna cewa waɗanda aka sauke zuwa ƙunƙashin ƙwaƙwalwa ko magungunan kulawa da gaggawa sun sauko da ƙimar kamuwa da cuta da kuma rage yawan mace-mace da tsawon lokacin asibiti.
Duk wani magani da zai iya sa TEN ya kamata a tsaya nan da nan. Ɗaya daga cikin binciken ya nuna cewa za a iya rage yawan mutuwar TEN ta kashi 5 zuwa 25 bisa dari idan an dakatar da shan magani mai tsanani bayan da farawa ya fara.
Sources:
Ngan, Vanessa. Manya-fatalwar epidermal necrolysis. Taimakon cututtukan jiki zuwa wakilan na waje. 26 Dec 2006 New Zealand Dermatological Society.
"Mai guba Epidermal Necrolysis." Skin Kumburi (Rashes). 31 Jan 2008 Jami'ar Maryland Medical Center.
Mai guba Epidermal Necrolysis. Rukunin Raunin Rare. Ƙungiyar Ƙungiyar Ƙananan Raunuka.
Medscape. "Maɗaukaki Epidermal Necrolysis" (2015).