Tsarin neutropenia na Cyclic shi ne yanayin da aka gaji inda kundin neutrophil (jini mai tsabta da ke yaki da cututtuka na kwayan cuta) ya zama ƙasa mai zurfi (yawanci kasa da 500 Kwayoyin / ML) a kan sake zagayowar kusan kowane kwana 21. Yawancin lokaci yakan gabatar a farkon shekara ta rayuwa. Hakan ya ragu da shekaru kuma zai iya ɓace a wasu marasa lafiya marasa lafiya.
Mene ne cututtuka?
Lokacin da ƙididdigar neutrophil na al'ada, babu alamun bayyanar.
Kwayoyin cututtuka kullum suna bar bayan neutropenia (ƙananan neutrophil ƙananan) ma'anar ƙididdigar neutrophil ya riga ya kasance da ƙananan ƙananan kwanaki kafin a ci gaba da bayyanar cututtuka. Rashin adawa ga sauran siffofin neutropenia (matsanancin tsaka-tsakin tsaka-tsaki, Shwachman Diamond Syndrome , da dai sauransu), ba a ganin lalacewar haihuwa. Kwayoyin cututtuka sun haɗa da:
- Aphthous ulcers (ulcers a bakin)
- Cire kumburi (pharyngitis)
- Gum ƙonewa (gingivitis)
- Cutar cututtuka
- Fever
Wane ne yake da hadari?
Tsarin neutropenia na Cyclic shine ainihin ma'anar cewa an haifi mutum tare da yanayin. An lalace a cikin iyalai a cikin wata hanya mafi girma da ke nuna cewa iyaye ɗaya ne kawai za a shawo kan su shigo da 'ya'yansu. Ba dukkanin iyalan dangi zasu iya shafar irin wannan ba kuma wasu na iya amma wasu bazai iya samun alamun bayyanar ba.
Yaya aka gano shi?
Tsakanin neutropenia na tsakiya zai iya zama kalubalanci don gano asali a matsayin mai tsauraran tsaka-tsaki kawai yana da kwanaki 3 zuwa 6 a kowane lokacin zagayowar.
Tsakanin waɗannan hawan keke, ƙididdigar neutrophil na al'ada ne. Rigakafi da kuma zazzabi na ci gaba a kowace kwanaki 21 zuwa 28 zai haifar da zato ga neutropenia na cyclic. Domin yunkurin sake zagayowar mai tsauraran tsaka-tsaki, cikakke jini (CBC) ana yin 2 zuwa sau 3 a kowane mako don makon 6 zuwa 8.
Bugu da ƙari da tsakaran tsaka-tsaki, za a iya ragewa a cikin kwayoyin jinin jini (reticulocytopenia) da / ko platelets (thrombocytopenia).
Ƙididdigar monocyte (wani nau'i na jini mai tsabta) yakan kara ƙaruwa a lokacin tsakaran tsaka tsaki.
Idan an yi tsammanin cewa kwayar neutropenia yana da ƙididdigar jini, an gwada gwajin kwayoyin don neman maye gurbin a cikin tsarin ELANE (a kan chromosome 19). 90 - 100% na marasa lafiya tare da neutropenia na cyclin suna da maye gurbin ELANE. Hanyoyi a cikin jinsin ELANE sun hade da neutropenia na cyclic da tsauraran tsaka-tsaki mai tsanani. Bisa ga gwajin gwaji da tabbatar da gwajin kwayoyin halitta, ba a buƙatar ɓangaren maniyyi na kasusuwan ba amma ba'a buƙata amma ana yin sau da yawa a lokacin aikin aikin neutropenia.
Menene Zabin Zaɓuɓɓuka?
Kodayake kwayar neutropenia na cyclic an dauke shi a matsayin mummunan yanayi, mutuwar na biyu zuwa manyan cututtuka sun faru. Jiyya yana aiki don hanawa da / ko magance cututtuka.
- Granulocyte Colony-Stimulating Factor (G-CSF, wanda ake kira mai ladabi): G-CSF ta ƙarfafa ƙashin kashi don samar da karin tsaka-tsaki. An yi amfani da shi don hana ƙididdigar neutrophil daga barin sama da 500 Kwayoyin / mL. An nuna G-CSF akan rage yawancin neutropenia kuma rage adadin cututtuka. G-CSF ana gudanarwa a ƙarƙashin hanya (a ƙarƙashin fata) a kowane kwanaki 1 - 2. Wasu marasa lafiya za su iya dakatar da G-CSF a matsayin mai tsufa saboda wani lokaci tsaka-tsakin neutropenia yana karuwa da shekaru.
- Maganin kwantar da hankalin rigakafi: Saboda yawancin cututtuka suna faruwa a cikin bakin, yana da muhimmanci a kula da tsafta mai kyau. Za a iya bada shawarar da za'a iya yin gyaran fuska na antibacterial.
- Bincike akan zazzabi: Saboda marasa lafiya tare da neutropenia na cyclic zasu iya haifar da cututtuka na kwayar cuta mai tsanani, yana da muhimmanci a yi nazarin zafin jiki a hankali. Wani lokaci, al'amuran zasu buƙaci samun asibiti tare da maganin rigakafi (IV) har sai kamuwa da cuta mai tsanani zai iya fita.