Zuciyar Zuciya a Haihuwa
Mafi yawan jini a cikin jiki kuma babban abinda ke dauke da jini daga zuciyarsa zuwa jiki shi ne hawan. A haɗuwa da aorta, zubar da zuciya a lokacin haihuwar haihuwa, wani ɓangare na alamar tana da mattatu (ƙuntatawa). Wannan ya sa ya fi wuya ga zuciya don zub da jini daga jiki.
Haɗin ƙwayar cutar yana faruwa a cikin kashi 5-8% na yara da aka haifa da ciwon zuciya (wanda ake kira cututtukan zuciya).
Yana faruwa sau biyu kamar sau da yawa a cikin yara kamar a cikin 'yan mata. Haɗin gwanin ya faru ne saboda jirgin bai bunkasa yadda ya dace ba a cikin makonni takwas na ciki. Wannan nakasar zuciya yafi kowa a cikin mutane da wasu cututtukan kwayoyin halitta irin su Turner syndrome . Yawanci ana gano shi a cikin yara da kuma manya a cikin shekaru 40.
Cutar cututtuka
Aorta tana kama da zane, tare da sashi mai lankwasa zuwa ga kai da kuma madaidaicin fili yana nunawa cikin jiki. Rashin haɗin dajin zai iya faruwa a ko'ina a cikin jirgin ruwa sai dai yana sa ran faruwa ne kawai bayan ƙwayar C-shaped a saman (da ake kira aortic baka). Wannan yana nufin cewa jini yana da wuya a lokacin fita daga jiki. Har ila yau, ƙin jini zai kasance babba a gaban sashen ƙuntataccen amma kasan bayan shi. Sabili da haka, yara tare da haɗuwa da hawan na iya samun alamun bayyanar kamar su:
- ciwon kai daga cutar hawan jini a kai
- ƙafar ƙafa ko kafafu
- cramps a kafafu tare da motsa jiki
- mahaukaciyar zuciya ta ji dadin zuciya (zuciyar zuciya)
- ƙaura ko faɗuwa
- Yara suna iya wahala wajen ciyarwa da wadataccen nauyi
Mafi tsanani ga ƙuntatawa, mafi tsanani kuma alamun bayyanar zai kasance. Ƙananan ƙuntatawa bazai haifar da bayyanar cututtuka ba.
Sanin asali
A wasu lokuta ana haɗuwa da ƙwayar aorta a lokacin jarrabawar jariri na farko ko a lokacin yin rajista tare da dan jariri.
Wasu lokuta cututtuka irin su murmurewa zuciya, ciwon kai, ko ƙananan hanyoyi zuwa kafafu zasu bada shawara akan ganewar asali. Kwararrun ƙwararrun yara ( likitan yara ) zai ba jaririn cikakken jarrabawar zuciya, ciki har da duba ƙwayar cuta da kuma karfin jini a cikin makamai da kafafu. A haɗuwa da aorta, bugun jini zai kasance mafi rauni kuma yaduwar jini a cikin kafafu fiye da cikin makamai.
Zane rayukan kirji na iya nuna ɓangaren kunkuntar aorta. Hanyar da za ta fi dacewa za ta zama dan haske na zuciya (echocardiogram). A cikin wannan hanya, likitan zuciyar mutum zai iya duba tsarin zuciya kuma ya ga haɗin da ke aorta. Wani lokuta wasu gwaje-gwaje irin su hoton da ke ciki (MRI) ko ƙididdigar hoto (CT) za'a iya buƙatar don tabbatar da ganewar asali.
Jiyya
Ana haɓaka ƙwayar aorta ta hanyar gyaran ɓangaren kunkuntar jirgin. Yawancin yara za su sami wannan gyara a jariri, kuma kusan dukkanin zasu gyara shi kafin shekaru 10. Akwai hanyoyi guda biyu da za'a iya gyarawa: ta hanyar angollasty balloon da kuma tiyata ta zuciya.
Balloon angioplasty - A cikin wannan hanya, an sanya mai mai zurfi tube (wanda ake kira catheter) a cikin babban jirgin jini a cikin karamin kuma ya kai ga zuciya zuwa inda aka raguwa aorta.
Cikakken yana da ƙananan ƙirar ƙira a ƙarshen shi. Lokacin da ya shiga ɓangaren kunkuntar, an nuna alamar taƙasa kuma an bude ɓangaren kunkuntar bude. Ƙananan na'urar da ake kira stent za a iya sanyawa a can don taimakawa a buɗe maɓallin.
Tiyata - An katse ragowar sashin aorta kuma an haɗa baki tare da lafiya. Idan ɓangaren da aka cire ya zama babban, anyi amfani da kayan roba ko ɗaya daga cikin jini na yaron don haɗuwa da rata.
Yawancin yara suna rayuwa mai kyau bayan gyaran haɗin gwiwa. Wasu lokuta lokacin raguwa na aorta zai sake faruwa. A wannan yanayin za a iya buƙatar angioplasty da kuma ƙarin tiyata don gyara shi.
Sources
> "Haɗin Aorta (CoA)." My Child Yana da asibitin yara Boston.
> Zieve, Dauda. "Ƙarfafawa daga cikin aorta." MedlinePlus Medical Encyclopedia. 11 Dec 2007. Ma'aikatar Magunguna ta {asar Amirka.