Zuciyar Zuciya a Haihuwa
Fassara daga cikin manyan arteries (TGA), wanda ake kira transposition daga manyan tasoshin, yana da mummunan zuciya wanda yake a lokacin haihuwa. A cikin wannan yanayin, matsayi na manyan jini guda biyu da ke dauke da jini daga zuciya, da ƙananan jini da ƙwaƙwalwar jini, an sauya su. An kiyasta cewa jigilar magunguna masu girma shine a cikin 1 a cikin 3,500-5,000 haihuwar, tare da yaran da ke shafar sau da yawa fiye da 'yan mata.
Ba'a san abin da ke haifar da TGA ba.
A cikin zuciya ta al'ada , jini daga jiki yana zuwa cikin zuciya kuma yana daga zuciya zuwa ga huhu ta hanyar yunkurin huhu don samun oxygen. Ya dawo cikin zuciya kuma ana fitar da shi ta jiki ta hanyar dabbar. Tun lokacin da aka canza rikici da kuma aorta a cikin TGA, jinin daga jiki ya shiga cikin zuciya amma dai ya sake dawowa jikinsa ba tare da zuwa ga huhu ga oxygen ba.
Magancewar manyan sutuna sau da yawa yakan faru da wasu cututtukan zuciya irin su ciwon sikila bakwai (VSD). A kashi 10 cikin dari na lokuta, akwai wasu nau'i-nau'i na haihuwa da suka kasance a cikin TGA.
Cutar cututtuka
Abubuwan da ke tattare da halayen maɗaukakiyar arteries sun kasance a lokacin haihuwar ko jimawa. Kwayoyin cututtuka sun haɗa da:
- Cyanosis - A TGA akwai isashshen oxygen kadan a cikin jinin da aka fitar dashi ga jiki. Yarinya yana da launi mai laushi ga fata ta kuma yana da rashin ƙarfi.
- Rawan numfashi da raunin zuciya
Yaya mummunar cututtuka sun dogara akan ko duk oxygen zai iya shiga cikin jini wanda aka fitar da jikinsa. Hanyoyin kwakwalwa na bakwai sune rami a bango a tsakiyar zuciya. Idan yana da shi zai iya bada izinin jinin da ke dauke da iskar oxygen a ciki don samun haɗuwa tare da jinin yana fita zuwa jiki.
A wannan yanayin, jaririn zai kasance da ƙwayar cyanosis, ko kawai yana da shi lokacin da yake kuka ko damuwa.
Sanin asali
Sakamakon ganewar asali na manyan arteries an tabbatar da shi ta hanyar duban zuciya, wanda ake kira echocardiogram . Idan TGA yana da tsammanin kafin haihuwa, za'a iya yin amfani da echocardiogram akan tayin a cikin mahaifa. Binciken da ake yiwa tsohuwar jigilar jini kafin haihuwa ya taimaka wajen tabbatar da cewa jaririn ya sami nau'in likita na musamman wanda zai bukaci bayan haihuwa.
Jiyya
Jimawa bayan haihuwar, jaririn da TGA zai fara samun magani mai magungunan (IV) da ake kira prostaglandin . Idan babu rami a cikin bango a tsakiyar zuciya don bada izinin jini tare da oxygen da za a hade tare da jini zuwa jikin, za a yi rami ta hanyar amfani da fasaha wanda ake kira balloon atrial septostomy (wanda aka sani da Rashkind hanya).
Wadannan jiyya, duk da haka, suna wucin gadi. Yaron zai buƙatar yin aikin tiyata don ya gyara zuciya, ya sa magungunan kwakwalwa da magungunan su koma cikin wuraren da suke dacewa (wanda ake kira gyaran haɓaka). Ana yin aikin tiyata a farkon watanni na rayuwar jaririn kuma ana iya buƙata a cikin makonni biyu na rayuwa idan cyanosis yana da tsanani.
Har zuwa tsakiyar karni na ashirin, yawancin jariran da aka haife su tare da fahimtar jita-jita mai girma ba su tsira fiye da 'yan watanni ba. Tun da sabuwar, mafi kyau dabarun aiki da kuma kulawa bayan aikin tiyata, hoton ya canza, kuma mafi yawan jarirai da TGA sun tsira ba tare da matsala masu tsanani ba.
Source:
> Martins, Paula, da Eduardo Castela. "Likita daga cikin manyan arteries." Labari na Orphanet na Rare Diseases 3 (2008): ePub.