Arrhythmogenic Daidaitan Ƙananan Cardiomyopathy - AVRC

Dalilin mutuwar 'yan wasa matasa a cikin kwatsam

Arrhythmogenic hakikanin ventricular cardiomyopathy (AVRC) wani yanayi ne wanda za'a iya maye gurbin muscle na zuciya da fibrous, nama mai mahimmanci, musamman a hannun dama ventricle. Babban dalili na AVRC yana da muhimmanci shi ne cewa zai iya haifar da arrhythmias na zuciya mai hatsari. (AVRC shine sunan "sabon" don wannan yanayin, wadda ake kira "dysplasia ventricular dama" arrhythmogenic.)

AVRC ba abu ba ne, amma ba mai ban sha'awa ba. Za a iya samuwa a cikin ɗaya daga cikin 2000 zuwa 5000 manya idan ka nemi shi. Duk da haka, kadai lokacin da jama'a ke ji game da AVRC shine lokacin da wani matashi yaro ya mutu ba zato ba tsammani, saboda AVRC na daya daga cikin yanayin zuciya da ke haɗuwa da mutuwar 'yan wasa .

Mene ne alamomi na AVRC?

Duk da yake AVRC wani cututtukan zuciya ne - wato, ƙwayar tsoka da ƙwayar zuciya - yana da wuya ya haifar da matsaloli masu tsoka wanda ya isa ya haifar da rashin zuciya . Maimakon haka, muhimmancin da yake da mahimmanci shi ne cewa zai iya haifar da arrhythmias cardiac - musamman, ƙananan kamfanonin ventricular, tachycardia ventricular , da kuma wani lokacin ventricular fibrillation .

Kwayoyin cututtuka da AVRC ke haifarwa suna danganta da haɗarin da zai iya haifarwa. Mutanen da ke tare da AVRC zasu kwatanta abubuwa da yawa na lalacewa , haske, ko syncope . Abin takaici, mutuwar kwatsam na iya faruwa, kuma mafi mawuyacin hali, mutuwar kwatsam na iya zama alama ta farko cewa akwai matsalar zuciya.

Duk da yake AVRC na iya haifar da mutuwar kwatsam a kowane lokaci, wannan taron zai iya faruwa a lokacin lokuta na motsa jiki. Wannan shi ne dalilin da ya sa AVRC na ɗaya daga cikin yanayin da ke haifar da mutuwar kwatsam kamar yadda yake da lafiya, matasa 'yan wasa.

Mutane da yawa tare da AVRC - har zuwa kashi 40% - ba za su sami alamun bayyanarwa ba, kuma ana bincikar su ne kawai lokacin da aka kula da su saboda cutar saboda an gano wani dan uwan ​​tare da shi.

Ta yaya aka gano AVRC?

Ana binciko bincikar AVRC ta nazarin electrocardiogram (wanda ke nuna wani tsari na musamman na QRS), da kuma echocardiogram (wanda ya nuna yawan halayen halayyar kirki a cikin ƙwayar zuciya na ventricle dama - kuma wani lokaci na ventricle hagu).

Idan ganewar asali ya kasance a cikin shakka, wani lokaci MRI na zuciya zai iya taimakawa abubuwan da ke ƙasa. Kwararrun kwayoyin zai iya taimakawa wajen samar da ganewar asali, kuma an bada shawarar ga duk mutanen da suke da wannan yanayin.

Duk da yake gwajin electrophysiologic zai iya taimakawa a wasu lokutan don taimakawa wajen gane ƙananan tachycardia saboda AVRC daga tachycardia ventricular da wasu yanayi na zuciya ke ciki, irin wannan gwajin ba yana taimakawa ba, kuma ba'a buƙata.

Da zarar an samo asali, za a kuma gwada nazarin halittu don dangi na farko. Game da ɗaya a cikin haɗin farko na farko na mutumin da ke tare da AVRC zai kuma ɓullo da wannan yanayin.

Biyan AVRC

Babbar manufar magance AVRC ita ce ta hana mutuwa daga zuciya ta zuciya daga tachycardia ventricular ko fibrillation.

Saboda mutuwar kwatsam yakan kasance tare da motsa jiki a cikin wannan yanayin, 'yan wasan da ke da AVRC ya kamata su guje wa dukkan wasanni masu gasa, tare da yiwuwar yin amfani da ƙananan ayyuka irin su golf ko bowling.

Bugu da ƙari kuma, ya kamata su guje wa kowane aiki da ke haifar da ƙananan alamu.

Abubuwan da ake kira arrhythmias da aka hade da AVRC sun fito ne ta hanyar motsa jiki mai tausayi - wani ɓangare na tsarin jiki mai kula da jiki wanda yana ƙaruwa matakan adrenaline, kuma yana da alhakin yaki ko amsawar jirgin. Wannan shine dalilin da yasa motsa jiki shine matsala tare da AVRC. Saboda haka, yawancin masu kwakwalwa suna bada shawara akan yin amfani da beta blockers a cikin wannan yanayin, don magance adrenaline a zuciya.

Ana ba da shawarar bada shawara ga mutane da dama tare da AVRC, musamman ga duk wanda ya taɓa yin ɓarna na kamacciyar zuciya, wani ɓangare na ciwon tachycardia na ventricular, wani ɓangare na syncope wanda bai dace ba, ko kuma wanda yake nunawa ya nuna yawancin ƙwayar ƙwayar zuciya.

Ga mutanen da ke tare da AVRC wadanda basu da waɗannan sharuɗɗa, haɗarin mutuwa ta kwatsam ya bayyana yana da ƙananan - muddin sun bi ƙuntatawar motsa jiki kuma suna ɗaukar beta blockers.

A cikin mutanen da ke tare da AVRC waɗanda suka ci gaba da maganin arrhythmias, ƙididdiga na tsawon lokaci yana da kyau sosai idan sun guje wa aikin motsa jiki, suyi beta blockers, karba da defibrillator wanda ba a iya sarrafawa, kuma (a wasu lokuta) sunyi amfani da magungunan antiarrthythmic .

Kalma Daga

Arrhyhythmogenic dama ventricular cardiomyopathy ne yanayin kwayoyin da zai iya haifar da yiwuwar na mutuwa cardiac arrhythmias, kuma yana daya daga cikin dalilai na mutuwar mutuwa a matasa 'yan wasan. Tare da jiyya mai tsanani, mutane da wannan yanayin sukan yi sosai.

> Sources:

> Al-Khatib SM, Stevenson WG, Ackerman MJ, et al. 2017 AHA / ACC / HRS Sharuɗɗa don Gudanar da marasa lafiya tare da Arrhythmias Ventricular da Rigakafin Mutuwar Cardiac Mutuwar: Tsarin Gida: Rahoton Cibiyar Kasuwanci ta Kasuwancin Amirka da Cibiyar Harkokin Kasuwancin Amirka ta Harkokin Kasuwancin Kasuwanci da Ƙungiyar Rhythm. Zuciya Zuciya 2017.

> Ruwald AC, Marcus F, Estes NA 3rd, et al. Ƙungiyar Ƙwallon Ƙasa Da Nishaɗin Harkokin Kasuwanci Tare da Kwayoyin Cardiac A Yanayin Magungunan Arrhythmogenic Dama na Cutar Cardiomyopathy: Sakamakon Daga Nazarin Hidima na Mujallolin Arewacin Arewacin Amirka na Arrhythmogenic Cardiomyopathy. Eur Heart J 2015; 36: 1735.