Myelofibrosis wani yanayi ne wanda ake sa fibrosis a cikin kututture. Wannan yunkuri yana da wuyar ƙwayar kasusuwa don yin jini a kullum.
Cutar cututtuka
Myelofibrosis na iya haifar da wani bayyanar cututtuka. Duk da haka, ana iya ɗauka akan aikin jinin na yau da kullum da likitanka ke yi. Sauran cututtuka suna da alaƙa da rage yawan jinin jini ( anemia ) da plalets ( thrombocypenia ), kamar:
- Wuci ko gajiya
- Pallor
- Jigon Red a fata da ake kira petechiae
- Ƙara murmushi
- Cutar jini mai tsanani
- Ƙarƙashin ƙwanƙara da / ko hanta - zaku iya lura da cikar da ke ƙasa da haƙarƙarinku.
- Bony zafi
- Fever ko m ciwo
Wanda ke da Hadarin
Myelofibrosis yakan kasance a cikin mutane fiye da shekaru 50. Yana iya faruwa a yara amma yana da wuya. Marasa lafiya tare da maganin polycythemia ko mahimmancin thrombocythemia zai ci gaba da bunkasa myelofibrosis.
Me ya sa yasa girmanka ya girma?
Jigon yana cikin kwayar hematopoietic, yana nufin cewa yana da damar yada jini. A cikin myelofibrosis, inda yatsun kasusuwan ke fama da wahalar yin jini, yarinyar ya kara girma don kokarin inganta aikin.
Dalilin
Myelofibrosis na farko shine wani nau'i na jini na jini (wani ɓangare na ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin cuta). Wannan ya haifar da maye gurbin kwayoyin halitta. A wannan lokaci ba mu tabbatar da abin da yake haifar da maye gurbin ba.
Myelofibrosis zai iya haifar da wasu yanayi kuma ana kiransa na biyu na myelofibrosis.
Wadannan sun haɗa da:
- Sauran ciwon jini, musamman m megakaryocytic cutar sankarar bargo (wani nau'i na m cutar mai sankarar myeloid ) ko myelodysplastic ciwo
- Canast metastasis zuwa kashi
- Cututtuka na Autoimmune kamar lupus, scleroderma
- Karuwar hawan jini na jini: A cikin wannan yanayin, akwai karfin jini a cikin jini a cikin huhu.
- Hyperparathyroidism hade da raunin bitamin D
- Abun ciwo na gilashi
- Renal ostoeodystrophy: Wannan mummunar cuta ne na ma'adinai da kashi wanda yake faruwa a marasa lafiya tare da cutar koda.
Sanin asali
Da farko, an ƙididdige jini ƙididdigar jini a ƙididdigar jini . Kullum, anemia da / ko thrombocytopenia suna nan. Rashin lalacewar jini yana iya ganewa a kan jinin jini, zane-zane mai zane na jini. Kwayoyin jini masu launin jinin sukan kasance suna kwatanta su kamar labarun.
Sakamakon asali na ƙarshe yana buƙatar ƙwayar maniyyi na kasusuwa, hanyar da za'a cire wani ƙananan kasusuwa. Tare da matakai na musamman, za'a iya gano nau'in fibrous a cikin kasusuwa.
A lokacin aikin bincike, likitanku zai gwada abin da ke haifar da myelofibrosis. Ya hada da wannan aikin zai zama gwajin kwayoyin ga wasu maye gurbin da aka kira JAK2, MPL, da CALR.
Jiyya
Jiyya yana dogara ne akan ainihin dalilin. Yin maganin myelofibrosis na farko yana ƙaddamar da haɗarin ci gaba da cutar da ci gaba da rayuwa.
- Kulawa: Idan baku da alamun bayyanar cututtuka, jiran jirage zai iya zama mafi kyawun magani.
- Harkokin jini : Anemia da thrombocytopenia da aka gani a cikin myelofibrosis na iya zama mai tsanani kuma yana iya buƙatar bugun jini sau da yawa. Yanayin karuwar jini zai iya ƙayyade idan ana buƙatar magani mai tsanani.
- Sashin sautin (tsire-tsire) sashi: Dole ne a yi la'akari da yankewa dashi a hankali a duba duka hadarin da kuma amfani.
- Ruxolitinib: Wannan magani yana hana JAK2 a cikin marasa lafiya tare da maye gurbin JAK2 wanda ke da alamun bayyanar cututtuka kuma basu cancanci karɓar launuka na kasusuwa ba.
- Splenectomy : Idan yarinyar ba ta rage yawanta daga magani ba, ana iya cire shi ta jiki.
- Hydroxyurea: Hydroxyurea wani magani ne na kwayar cutar shan magani wanda za'a iya amfani dasu don rage girman ƙwayar da sauransu.
- Wasu magunguna kamar inrogene da thalidomide
- Za'a iya amfani da farfadowa na radiation don rage yawan ƙwanƙolin
Jiyya ga sakandare na myelofibrosis an umurce shi ne a kan mahimman abu. To, idan myelofibrosis ya haifar da ciwon daji irin su mikiloid cutar sankarar bargo (AML), ana bi da shi tare da chemotherapy. Idan myelofibrosis ya zama na biyu zuwa wani nau'in mikiya, mai kula da wannan cuta zai iya inganta yawan jini.
Duk abin da magani, kungiyar likita za su biye ku ta duk matakan da kuke buƙatar ɗauka don kula da lafiyarku. Kada ku yi shakka ku raba tunaninku, tambayoyinku, da kuma ji da su.