Cutar da ke Rare wanda ke haifar da maganin numfashi
Kartagener syndrome, wani cututtuka ne mai yawan gaske wanda ke haifar da lahani a cikin kwayoyin . Yana da jinkiri , ma'anar cewa kawai yakan faru ne idan iyaye biyu suna dauke da kwayar. Kartagener ciwo yana shafar kusan mutane 30,000, ciki har da dukkan genders.
An san shi don manyan abubuwan da ke maƙasudin su guda biyu: ƙananan dyskinesia ciliary da kuma situs inversus.
Ciliary Dyskinesia
Hanyoyin numfashi na mutum sun hada da hanci, sinuses, kunnen tsakiya, tubes na eustachian , makogwaro, da kuma numfashi mai zurfi ( trachea , bronchi , and bronchioles ). An haɗa dukkanin sashin jiki tare da ƙwayoyin da ke da nau'i mai kama da gashi, wanda ake kira cilia. Cilia ta yalwata kwayoyin ƙurar ƙura, hayaki, da kuma kwayoyin cuta kuma daga cikin sutura.
A cikin yanayin dyskinesia na ciliary da ke hade da Kartagener Syndrome, ƙwararrun ba su da kyau kuma basu aiki daidai. Wannan yana nufin cewa ƙwayoyin ƙwayoyin cuta da kwayoyin cuta a cikin huhu ba za a iya fitar da su ba, kuma sakamakon haka, cututtuka na huhu, irin su ciwon huhu, ci gaba.
Cilia ma a cikin ventricles na kwakwalwa da kuma a cikin tsarin haihuwa. Mutanen da ke fama da cutar Kartagener na iya ciwon kai da matsaloli tare da haihuwa.
Shafukan yanar gizo
Sakamakon situs yana faruwa yayin da tayin ke cikin ciki. Yana sa gabobin su bunkasa a ɓangaren ɓangaren jiki, suna sauyawa matsayi na al'ada.
A wasu lokuta, dukkanin kwayoyin halitta na iya zama madubi na siffar matsayi na al'ada, yayin da a wasu lokuta, ana gyara wasu gabobin musamman.
Cutar cututtuka
Yawancin alamun bayyanar cututtukan kartagener sakamakon sakamako daga rashin iyawa na numfashi na numfashi don aiki daidai, kamar:
- Binciken sinus na yau da kullum
- Kwayoyin cuta na yau da kullum, irin su ciwon huhu da mashako
- Bronchiectasis - cutar lalacewar daga cututtuka masu yawa
- Sauran kunnuwan kunnen baki
Muhimmiyar alama wadda ta bambanta ciwon kartagener daga sauran nau'in dyskinesia ciliary na farko shine matsayi na gabobin ciki a gefe da ke gefe da na al'ada (wanda ake kira situs inversus). Alal misali, zuciya yana gefen dama na kirji maimakon hagu.
Sanin asali
Karugener ciwon da aka gane ta uku manyan alamun bayyanar cutar sinadaran, bronchiectasis da kuma situs inversus. Rawan x-rayuka ko ƙididdigar rubutu (CT) za su iya gano cutar daji na halayyar ciwo. Yin amfani da kwayar halitta na sutura, ƙwayar cuta ko sinuses na iya bada izinin binciken kwayoyin halitta wanda ke haifar da respiratory tract, wanda zai iya gano alamar cutar.
Jiyya
Kula da lafiyar mutumin da ke fama da ciwon Kartagener yana mai da hankali ga rigakafin cututtuka na numfashi da kuma magance duk wani abu da zai iya faruwa. Alurar rigakafi na iya taimaka sinusitis, da kuma shayarwa da magunguna da kuma numfashi na numfashi na iya taimakawa idan cutar ta ci gaba da tasowa. Ana iya sanya ƙananan rami a cikin eardrums don ba da damar ciwo da ruwa don fitarwa daga tsakiyar kunne. Matasa, musamman ma maza, suna iya fuskantar matsala tare da haihuwa kuma zasu iya amfana daga tuntuɓar likita na haihuwa. A lokuta masu tsanani, wasu mutane na iya buƙatar cike da sutura.
A yawancin mutane, adadin cututtuka na numfashi ya fara karu da kimanin shekaru 20, kuma sakamakon haka, mutane da yawa da ke fama da cutar Kartagener suna kusa da al'ada na al'ada.
Source:
"Mene ne Ciliary Dyskinesia?" Ƙungiyar PCD . 24 Nuwamba 2008
Rice, S. "Kartagener Ciwo". Healthline , 2013.