Dancing Feet Dancing Dancing
Opsoclonus-myoclonus syndrome (OMS) wata cuta ce mai ciwo mai ban ƙyama. Yana haddasa al'amurra masu mahimmanci tare da basirar motar, motsa ido, hali, rikice-rikice na harshe da matsalolin barci. Ya sau da yawa sau da yawa ba zato ba tsammani kuma yana da yawanci kullum; idan an gano ku tare da ciwo na opsoclonus-myoclonus, zai yiwu a cikin rayuwarku duka.
Sunanta yana bayyana alamunta: opsoclonus shine motsi ido da kuma myoclonus yana nufin haɗuwa da ƙwayar tsoka. Har ila yau an san shi da "Kinsbourne syndrome" ko "dancing-eyes-dancing-feet".
Wanda ke cikin Hadarin
A cikin rashin lafiyar jiki , jiki yana kaiwa jikinsa lafiya. Opsoclonus-myoclonus ciwon yana haifar da cutar ta jiki wanda jikin jikin ya ke amsawa ko dai kamuwa da kamuwa da cuta ko kwayar da ake kira neuroblastoma. A cikin kowane hali, magungunan sun ƙare magungunan ƙwayoyin kwakwalwa, kuma wannan yana haifar da lalacewa wanda ya haifar da alamar cututtuka.
Opsoclonus-ciwon maganin myoclonus yakan faru sau da yawa a cikin yara. Yara jarirai sune shekarun da yawancin neuroblastoma ke tasowa; game da kashi hudu cikin dari na waɗannan yara za su ci gaba da OMS. Duk wani jariri wanda ke da OMS zai jarraba don ganin ko ta kasance da ciwon tumo, ko da yake yana da lafiya tare da kamuwa da cutar ta hanyar bidiyo mai bambance-bambance tun lokacin da sau biyu ke tafiya tare.
Jiyya
Babban damuwa da opsoclonus-myoclonus ciwo shine farkon asali da jiyya domin cimma burin gyarawa da sake dawowa. Idan yarinya yana da ciwon ƙwayar cuta na myoclonus kuma yana da ciwon ƙwayar cuta, ana yawan cire macijin ƙwayar jiki. Yawancin lokaci, ciwon sukari yana cikin matakan farko kuma ba a buƙatar maganin cutar shan magani ko radiation.
Wani lokaci wannan yana inganta ko kawar da bayyanar cututtuka. A cikin tsofaffi, ƙullun cire sau da yawa baya taimakawa kuma alamun cututtuka na iya kara muni.
Sauran jiyya sun haɗa da:
- Adonocorticotrophic hormone (ACTH) injections
- Intravenous immunoglobulins - shirye-shiryen kasuwanci na antibodies daga masu lafiya mai bayar da lafiya lafiya
- Azathioprine (Imuran) - yana kawar da tsarin rigakafi, wanda ya rage jinkirin samar da kwayoyin cuta
- Magungunan maganganun maganganu da na intravenous, irin su prednisone, dexamethasone, da hydrocortisone
- Chemotherapy kamar cyclophosphamide da methotrexate, ga yara da neuroblastoma
- Kwararrun ilimin likitanci - musayar jini jini
- Anyi amfani da rigakafi - tsaftace tsararrun kwayoyin cutar daga cikin jini a cikin manya tare da OMS.
Maganganun ci gaba da ake buƙata don ci gaba da gudanar da alamun bayyanar cututtuka kuma rage haɗarin ƙwayar cutar.
Faɗakarwa
Mutanen da ke da damar da za su dawo a al'ada bayan jiyya su ne wadanda ke da alamar bayyanar cututtuka. Wadanda ke da alamun bayyanar cututtuka na iya samun taimako daga ɗaukar ƙwayar tsoka (myoclonus) amma suna da matsala tare da daidaituwa. Sauran matsalolin da ke fama da rauni daga kwakwalwa, irin su ilmantarwa da matsalolin hali, rashin kulawa da rashin kulawa da hankali (ADHD) da rikice-rikice-rikice, na iya faruwa, kuma waɗannan na iya buƙatar nasu jiyya.
Yara da ke da alamun cututtukan OMS mafi tsanani suna iya samun lalacewar kwakwalwa na yau da kullum wanda zai iya haifar da nakasa ta jiki da ta jiki.
Tsarin jima'i
Opsoclonus-Ciwon ƙwayar Myoclonus yana da wuya; kawai mutane 1 ne kawai aka yi imani da cewa suna da batun a duniya. Yawanci yana ganin yara da manya, amma zai iya rinjayar manya. Yana faruwa sau da yawa a cikin 'yan mata fiye da yara maza kuma yawanci ne kawai aka bincikar bayan an sami watanni 6.
Sources:
Pranzatelli, M. "Alamar da ke ciki: Wuta mai kyau." Discove r, 2000.
Pranzatelli, M. "Opsoclonus-Myoclonus Syndrome". Ƙungiyar Ƙungiya ta Ƙananan Raunuka, 2016.