VACTERL Rahoton Haihuwa Aiki Tare
Maganar VACTERL tana nufin wani ɓangare na lalacewar haihuwa da ke faruwa tare; wadannan halayen suna da alaƙa kuma suna faruwa ta hanzari, suna shafi sassa daban-daban na jiki. Ƙungiyar VACTERL na iya haifar da alamun alamun da yawa, don haka ba a san yawan yara ba. Halin zai iya faruwa tare da wasu cututtuka na chromosome kamar Trisomy 18 (Edwards syndrome), ko a cikin yara na iyaye masu ciwon sukari , amma ainihin dalilin ba a sani ba; yana iya haifuwa ta hanyar haɗuwa da abubuwan da ke tattare da muhalli da kwayoyin halitta.
Ƙungiyar VACTERL tana da wuya sosai, yana da tasiri kamar 1 a cikin haihuwa 40,000.
Cutar cututtuka
Kowace wasika a VACTERL tana wakiltar wasika na farko na alamun bayyanar ta. Ba duk yara da VACTERL ke haɗuwa ba suna da waɗannan hauka.
- V yana tsaye ne ga ƙwanƙwasa (kasusuwa na kashin baya), waɗanda suke da hauka
- A tsaye ne a kan tsararru mai tsauri ko wani abu wanda ba shi da tushe, ma'ana anus ne wanda ba ya bude waje
- C na nufin cututtuka na zuciya (zuciya), yawanci wani ramin mahaukaci tsakanin sassan zuciya (gurgunin ƙwararrun ƙwararrun ƙwayar cuta ko gurɓatattun lahani)
- T yana tsaye ne a kan fistula na tracheoesophageal, ma'ana an haɗuwar haɗuwa a tsakanin trachea (windpipe) da esophagus (jaririn abinci ga ciki)
- E tsaye ga atresia atresia, ma'anar cewa esophagus ba ya haɗa da ciki
- R yana tsaye ne saboda ƙananan ƙwayar koda ( koda )
- L yana tsaye a kan ƙananan ƙafa (ƙarfin hannu) kamar yatsun da ba a ciki ba, wasu yatsunsu (polydactyly), yatsun yatsunsu (mahaukaci), ko kashi wanda ya rasa a hannunsa ko kafafu
Wasu jariran da aka haife su tare da ƙungiyar VACTERL suna da nauyin ɗayan ɗayan ɗalibai kawai (maimakon al'ada biyu). Yawancin jarirai an haife ƙananan kuma suna fama da wahala kuma suna samun karfin.
Sanin asali
Sanin asali na ƙungiyar VACTERL ya dogara ne akan lahani na haihuwa. Babu wani gwajin da ake bukata don tabbatar da ganewar asali.
Wasu matsalolin, irin su wani ɓangaren ƙafa ko wasu yatsunsu, za a gano lokacin da aka jariri jariri bayan haihuwa. Harkokin X-rayayyi, makamai, da ƙafafu zasu iya gano ƙananan kasusuwa. Kwafar ƙwaƙwalwa (ƙwaƙwalwar zuciya) zai iya gane ƙwayar zuciya. Wasu gwaje-gwaje za a iya yi domin gano yiwuwar atresiaal atresia da fartulasal fistula ko cutar koda.
Jiyya
Kowace yanayin tare da ƙungiyar VACTERL na da cikakkiyar mahimmanci kuma mai yiwuwa ga jiyya da ƙwarewa yana dogara ne akan halin mutum. Ana biyan yanayin a kan kowane mutum; ba a halicci tsari na duniya don VACTERL ƙungiyar ba. Wasu haukarori suna da tsanani sosai magani ba zai ci nasara ba kuma jariri mai cutar ba zai tsira ba. A wasu lokuta, tiyata zai iya iya gyara lahani, ba da damar yaron ya rayu kuma ya rayu a rayuwa mai mahimmanci.
Da zarar an gano lahani na haihuwar haihuwa, za'a iya tsara tsarin kulawa ga jariri. Wasu matsalolin, irin su atophageal atresia, fartula, faulula, ko ƙwayar zuciya, na iya buƙatar likita ko aikin tiyata nan da nan. Wani lokacin tiyata don gyara matsalar zai iya jira har yaron ya tsufa. Sau da yawa, masu sana'a da yawa suna cikin kulawa da yaron tare da ƙungiyar VACTERL.
Yara da ke da hannu, kafafu, ko matsaloli na kashin baya zasu iya buƙatar aikin jiki ko aikin.
Sources:
"VACTERL Association". BirthDefects.org, 2015.
Castori, M. "VACTERL Association". Ƙungiyoyin Ƙungiyoyi don Raunuka marasa lafiya, 2016.