Abun kula da fasalin fasalin sune rukuni na rikici na jini inda wuraren da ba su yi aiki ba daidai ba, suna haifar da zub da jini. Wadannan cututtuka za a iya gaji (aka raba a cikin iyalai) ko samuwa (ci gaba a baya).
Mene ne alamun cututtuka na Yanayin Sakamakon Farawa?
Platelets wani bangare ne na tsarin gudanarwa, tsarin da zai taimake mu dakatar da jini.
Idan plalets ɗinku ba suyi aiki ba daidai ba, kuna da ƙari na jini. Kwayar cututtuka na iya haɗawa da:
- Ƙara murmushi
- Hanciyar nama
- Gum na jini
- Menorrhagia (matsanancin zubar jini)
- Zubar da zub da jini bayan an yanke ko wasu rauni
- Tsawon zub da jini tare da tiyata
Abin da ke haifar da Raunin Sakamakon Filato?
Za'a iya raba raunin aiki na kamfanoni zuwa manyan manyan nau'o'i biyu: haɓaka (gado) ko samu. Yawancin cututtuka sune marasa lafiya, ciki har da:
- Glanzmann ta thrombasthenia
- Binciken Bernard-Soulier
- Abun ciwo na gilashi
- Rashin lafiya na MYH9: May-Hegglin anomaly, ciwo na Epstein, Fechtner ciwo, da ciwo na Sebastian
- Sakamakon Wiskott-Aldrich: Wannan ciwo ne na rashin daidaituwa da ƙananan platelets. An bayyana shi da kananan plalets (mafi yawan kayan aiki na platelet suna da al'ada ga manyan plalets).
- Chediak-Higashi ciwo
- Hermansky-Pudlak ciwo
Abubuwan da aka samo sun hada da:
- Magunguna: Magunguna kamar aspirin, dipyridamole (Persantine), da clopidgrel (Plavix) an tsara don rage aikin platelets. Ibuprofen kuma yana rage yawan tasirin plalets amma ya rage aspirin.
- Cutar cutar
- Uremia (mummunar cututtuka)
- Myeloproliferative cuta kamar na da muhimmanci thrombocythemia
Ta Yaya Raunin Kwayoyin Firayi Ne aka gano?
Sakamako ga wasu nau'o'in plalet, waɗanda sukan kasance tare da lambar plalet (mafi girma ko ragewa), nau'in aiki na platelet na iya ƙididdigar adadi na al'ada.
Sauran nau'ikan nau'in cuta na platelet na iya samun thrombocytopenia , ko ƙididdigar platelet. Ya kamata a sake gwada takalma a karkashin na'urar microscope a jikin jini. Da dama daga cikin nau'in abin da ke tattare da farantin abin da ke cikin layi na haifar da waxanda suke da girma fiye da al'ada. Sauran suna ɓacewa ɓangaren magunguna na plalets, wanda ake kira granules, wanda za'a iya gani. Wani lokaci plalets ne na al'ada a cikin bayyanar da girman.
Sauran aikin gyare-gyare zai fara kama da sauran ciwon jini. Rashin amincewa da hemophilia (wani ɓangaren halayen coagulation), gwaje-gwajen gwaje-gwajen kamar lokaci na prothrombin (PT) da kuma lokaci na thromboplastin (PTT) na al'ada. Binciken gwajin kayan aikin platelet yana buƙatar gwaji ta musamman. Da ke ƙasa akwai jerin gajeren jerin gwaje-gwajen da aka yi amfani dashi.
- Lokacin jinkiri: Wannan gwaji ba a la'akari da shi ba ne game da rashin aiki na platelet kuma sabili da iyakokin gwaji ba a la'akari da gwaji mai kyau na tsarin clotting ba.
- Taswirar Platelet gwagwarmaya: Wannan yana dauke da mutane da yawa don zama kyakkyawan gwajin gwajin gwajin gwaji. Wannan gwajin yana shafar ƙididdigar platelet kuma mai yiwuwa ba daidai ba idan kuna da ƙananan platelet.
- Gwajin gwaje-gwaje na gwaje-gwaje: Wannan gwajin yayi la'akari da yadda talikan ke jimre wa juna (kungiya) don amsa matsalolin daban-daban. Ana iya amfani da wannan gwaji don auna tasirin aspirin ko clopidogrel (Plavix) farfadowa.
- Tsarin lantarki mai kwakwalwa: Wannan hanya ce ta musamman don dubi platelets tare da ƙananan microscope wanda zai iya ganin ɓangaren sassa na platelet.
Mene ne Hanyoyi?
Jiyya yana dogara ne akan irin nauyin aiki na platelet wanda kake da ita. Wasu ayyuka na platelet da wuya suna bukatar magani sai dai idan kun ji rauni ko buƙatar tiyata.
- Aspirin da NSAIDs: Ku guje wa aspirin ko wadanda ba masu steroidal anti-inflammatory (NSAIDs) kamar ibuprofen. Wadannan magungunan sun rage aiki na platelets wanda zai iya kara haɗarin jini.
- Magunguna masu haɗari: Kamar sauran cututtuka na zubar da jinin jini mai tsanani, ana iya amfani da rigakafi na hormonal don ci gaba da zubar da jinin mutum zuwa mafi ƙarancin.
- Magungunan maganin anti-fibrinolytic: Domin yana iya zama da wuya ga jiki don yin kwanciyar hankali, musamman ma a kan jikin mucosa (bakin, hanci, da dai sauransu), magungunan antifibrinolytic kamar Amicar ko Lysteda za'a iya amfani da su don dakatar da jini. Wadannan magunguna suna amfani dasu a cikin wadannan yanayi na hanci, da zubar da jini, da kuma menorrhagia. Hakanan za'a iya amfani da su bayan ƙwayoyin aiki (musamman, baki, hanci, da wuya) don hana zub da jini.
- Fassara na Platelet: Ko da a cikin yanayin aiki na platelet tare da ƙididdigar ƙwallon ƙafa na al'ada, ana iya amfani da ƙwayar platinet don jini mai tsanani ko kuma idan kana bukatar ka je aikin tiyata.
- Factor VIIa (NovoSevenRT) jiko: Wannan samfurin maye gurbin zai iya amfani dashi a wasu marasa lafiya tare da rashin aiki na platelet. An yi amfani da wannan a mafi yawan marasa lafiya wadanda basu iya karɓar raunin platin transfusions a matsayin wani zaɓi na maganin.