Cutar cutar cututtuka
Magungunan ciwon haɗin gwaninta (MCTD) wata cuta ce da ke dauke da nau'in cututtuka uku na haɗin haɗin linzamin kwamfuta - lupus erythematosus , scleroderma , da polymyositis.
Dalilin
Ba a san hanyar MCTD ba. Kimanin kashi 80 na mutanen da aka gano tare da MCTD mata ne. Kwayar ta shafi mutane daga shekaru 5 zuwa 80 tare da mafi girma a tsakanin matasa ko mutane a cikin shekaru 20.
Akwai yiwuwar jigilar kwayoyin halitta amma ba a kai gadon kai tsaye ba.
Cutar cututtuka
Sakamakon farko na cututtuka masu haɗuwa da haɗin gwiwa sune kamar bayyanar cututtukan da ke hade da wasu cututtuka masu haɗi na haɗi kuma zasu iya haɗawa da:
- Wulo
- Ciki mai rauni ko rauni
- Haɗin gwiwa
- Low-sa zazzabi
- Tarihin Raynaud
Kwayoyin cututtuka da suka haɗa da MCTD sun hada da polymyositis mai tsanani (mafi yawancin ke shafar kafadu da babba na sama), ciwo mai karfin ciwon maganin arthritis, manceitis mai tsauri, myelitis, gangrene na yatsunsu da yatsun kafa, babban zazzabi, ciwon ciki, rashin tausayi na jijiyar cututtuka a fuska, wahala a haɗuwa, rashin ƙarfi na numfashi, da kuma asarar sauraro. Labaran suna da tasiri har zuwa kashi 75 na mutanen da ke tare da MCTD. Kimanin kashi 25 cikin dari na marasa lafiya tare da MCTD suna da hannu a koda.
Sanin asali
Samun maganin cututtuka mai haɗuwa mai haɗin gwiwa zai iya zama da wuya. Hanyoyi na yanayin uku-lupus erythematosus, scleroderma, da polymyositis-yawanci ba su faruwa a lokaci ɗaya.
Maimakon haka, suna yawan ci gaba daya bayan wasu a tsawon lokaci.
Amma, akwai wasu abubuwa hudu da zasu bayar da shawarar ganewar asali na MCTD maimakon nau'in cuta mai haɗa kai:
- Babban haɗari na anti-U1 RNP (ribonucleoprotein) cikin jini
- Rashin wasu al'amurran da suka shafi kwayoyin lupus erythematosus, kamar matsaloli na koda da kuma matsalolin tsarin kulawa da tsaki
- Babban cututtuka da ciwon jini na jini (ba na kowa a cikin lupus ko scleroderma)
- Hanyar Raynaud, da kuma hannayen kumbura (ba mabambanta ba ne tare da lupus na tsarin jiki)
Duk da yake kasancewa da U1 RNP shine ainihin haɓakaccen halayyar da ke tattare da ganewar asali na MCTD, kasancewar mai cike da jini a cikin jini zai iya haifar da bayyanar cututtuka.
Jiyya
Yin jiyya na cututtukan nama na haɗin gwiwar da aka haɗa don kula da bayyanar cututtuka da kuma kula da mummunan cututtuka na cutar, irin su shigarwar kwayoyin. Alal misali, hawan jini na jini ya kamata a bi da shi tare da magunguna masu guba. Kwayoyin cututtuka na inflammatory na iya kasancewa daga m zuwa mai tsanani, kuma za a zafin zafin jiki bisa ga tsananin. Don ƙananan ƙonewa, za a iya ba da NSAIDs ko ƙananan corticosteroids . Ƙananan kisa mai tsanani zai iya buƙatar matsanancin corticosteroids. Lokacin da aka aiwatar da kwayoyin halitta, za'a iya ba da umarnin maganin immunosuppressants.
Outlook
Ko da tare da cikakkiyar ganewar asali da magani mai dacewa, ƙwarewar iya zama da wuya a tsara. Yaya lafiyayyi ya dogara ne akan irin gabobin da suke ciki, da mummunan kumburi, da cigaba da cutar. A cewar Cleveland Clinic, kashi 80 cikin dari na mutanen da ke rayuwa kimanin shekaru 10 bayan an gano su tare da MCTD.
Mahimmancin ga MCTD ya kasance mafi muni ga marasa lafiya da halaye waɗanda aka danganta ga scleroderma ko polymyositis.
Yana da muhimmanci a lura cewa za'a iya samun karin lokaci wanda ba shi da alamar rashin lafiya, ko da ba tare da magani ga MCTD ba.
> Sources:
> Bennett R. Anti-U1 RNP Antibodies a cikin Haɗakarwar Haɗakarwar Haɗakarwar cuta. Na zamani.
> Firestein GS, Kelley WN. Kelleys Textbook na Rheumatology . Philadelphia, PA: Elsevier / Saunders; 2013.
> Gunnarsson R, Hetlevik SO, Lilleby V, Molberg Ø. Mixed nama mai launi. Best Practice & Nazarin Clinical Rheumatology . 2016; 30 (1): 95-111. Doi: 10.1016 / j.berh.2016.03.002.
> Ƙungiyar Haɗayyar Maɗaukaki Mixed. Cleveland Clinic.