Lymphangiomatosis da Lymph System

Lymphangiomatosis wani cuta ne wanda yawancin ciwace-ciwacen kwayoyi (lymphangiomas) ko cysts suke girma cikin tsarin lymph na jiki. Ko da yake waɗannan ciwace-ciwacen ba su da magungunan, sun mamaye kyallen takalmin jiki kuma suna haifar da ciwo, wahalar numfashi, da kuma sauran cututtuka dabam dabam dangane da inda suke faruwa. Lymphangiomas na iya girma cikin kasusuwa, kayan haɗin kai, da kuma gabobin jiki, kuma zasu iya katsewa, damfara, ko halakar kyakyawa.

Abin da ke haifar da lymphangiomatosis bai riga ya sani ba.

Lymphangiomatosis ne mafi yawancin kamuwa da cutar a jariri da yara ƙanana amma zai iya faruwa a kowane zamani. Yana shafi maza da mata na kowane kabila. Saboda lymphangiomatosis yana da wuya kuma yana da wuyar ganewa daidai, ba a san yadda yawancin mutane suke shafar shi ba a duk faɗin duniya.

Cutar cututtuka

Alamar cututtuka na lymphangiomatosis na dogara akan inda ciwon sukari ke girma a jiki.

Yawan lokaci, daya ko fiye kasusuwa zai iya maye gurbin kwayar lymphangioma, wanda aka sani da cutar Gorham. Lymphangiomas ba su girma cikin kwakwalwa saboda tsarin lymph ba ya zuwa cikin shi.

Sanin asali

Sakamakon ilimin lymphangiomatosis ya dogara ne akan bayyanar cututtuka da kuma kasancewar yawan lymphangiomas a jiki. CT (ƙididdigar rubutun kwaikwayon) da nazarin fuska mai haske (MRI) ana amfani dasu don kimanta cutar. An dauki samfurin nama (biopsy) don taimakawa tabbatar da cewa ciwon sukari ne lymphangiomas.

Jiyya

Lymphangiomatosis sannu-sannu yana damuwa a kan lokaci. Yayin da ciwon sukari ya girma, zasu iya haifar da bayyanar cututtuka, wasu daga cikinsu na iya zama barazanar rai, kamar haddasa ruwa don tattarawa a cikin huhu wanda ya hana numfashi. Zubar da kututture mai sauƙi yana yiwuwa, amma wasu ciwace-ciwacen ƙila zai zama da wuya a cire gaba ɗaya idan sun yada. Wani magani da ake kira Intron A (interferon alfa), chemotherapy, ko radiationrapy zai iya taimaka wajen magance cutar. Sauran jiyya ko jinya zai iya taimakawa wajen kawar da wasu daga cikin bayyanar cututtuka ko matsalolin da lymphangiomatosis ke haifarwa. Alal misali, za'a iya saka tube a cikin akwati (thoracentesis) don cire ruwa mai kwakwalwa, ko kuma a tilasta aikin tiyata a kan spine don taimakawa jijiyoyi.

Sources:

> "Game da Lymphangiomatosis." Lymphangiomatosis & Gorham ta cuta Alliance. 06 Sep 2007. Lymphangiomatosis & Gorham's Disease Alliance.

> Marom, Edith, Cesar Moran, & Reginald Munden. "Karkataccen Lymphangiomatosis." Jaridar American Journal of Roentgenology 182 (2004): 1068.

> Rostom, A Y. "Jiyya na thoracic lymphangiomatosis." Maganganun Cututtuka a Ƙananan yara 83 (2000): 138-139.