Bayani
Kodayake kalmomi na iya zama abin firgita, Erythroblastopenia na Ƙananan yara (TEC) ita ce iyakacin iyakar yara. Wannan shi ne dalilin da ya fi dacewa don rage yawan kwayar jini a cikin yara. Erythroblasts sune kwayoyin dake samar da jini a jikin jini da jini-daga cikin kalmar Helenanci don rashi. Mafi mahimmanci, anemia zai haifar da rashin yiwuwar ƙwayar kasusuwa don samar da jinin jinin dan lokaci.
Cutar cututtuka
Anemia a TEC yana da jinkiri saboda haka wasu yara ba su da alamun bayyanar. Wadannan yara za a iya samo su a wani lokaci tare da aikin jini na yau da kullum ko kuma zasu iya dawowa ba tare da samun zuwan likita ba. A wasu marasa lafiya, alamun cututtuka suna da dangantaka da anemia. Sun hada da:
- Wuci ko gajiya
- Pallor ko kodadde fata
- Dizziness
- Rafin zuciya mai sauri, wanda ake kira tachycardia
- Rawancin numfashi
Rick Factors
Kamar yadda sunan ya nuna, TEC yana faruwa a lokacin yaro. Yawancin yara ana bincikar su tsakanin shekara daya da hudu. Yara suna nuna kara yawan haɗari idan aka kwatanta da 'yan mata.
Sanin asali
Babu gwajin gwaji guda daya na TEC. Wasu marasa lafiya za a iya gano su ta hanyar aikin jini na yau da kullum don kula da yara. A wasu marasa lafiya, idan ana zargin anemia, ana gano TEC a cikakken ƙididdigar jini (CBC). Gaba ɗaya, CBC zai bayyana alamar anemia. Lokaci-lokaci akwai neutropenia (ƙananan tsakaicin tsaka-tsaki, wani nau'i na jini mai tsabta).
Kwayoyin jini na jini suna da yawa amma ana iya kara girma lokacin da mai haƙuri ya fara dawowa.
Kashi na gaba na aiki shine kididdigar reticulocyte. Magunguna sunadaran jini ne kawai wanda aka saki daga kasusuwa. Da farko dai, ƙididdigar reticulocyte ne, wanda ake kira reticulocytopenia.
Da zarar maye gurbin ɓarwar kashi ya yi nasara, ƙididdigar reticulocyte sama (mafi girma daga al'ada) don sake sake yaduwar jini kuma ya dawo cikin al'ada lokacin da anemia ta warware.
A lokacin aikin aiki, yana da mahimmanci a rarrabe TEC daga Diamond Blackfan Anemia (DBA), wanda aka gaji da anemia. Abokan da ke tare da DBA suna da ciwo mai tsanani. Abokan da ke da DBA su ne ƙananan ƙananan (a cikin shekaru 1) a ganewar asali kuma jinin jinin ya fi girma fiye da na al'ada (macrocytosis). Ba da daɗewa ba, idan ganewar asali ba a bayyana wani yunkuri mai laushi da kuma biopsy na iya buƙata a yi. Wani lokaci gwajin tabbatarwa mafi kyau ga TEC shi ne cewa mai lafiya ya dawo ba tare da yin magana ba.
Dalilin
Amsar amsar ita ce ba mu sani ba. Kimanin kashi daya cikin rabi marasa lafiya za su bayar da rahoton wata cuta mai cututtukan jini 2 - 3 watanni kafin ganewar asali. An yi tsammanin cewa kwayar cuta ta haifar da maye gurbin lokaci na yaduwar jini a cikin kasusuwa. Yawancin ƙwayoyin cuta an haɗa su tare da TEC amma babu wanda ya dace.
Duration
A mafi yawan lokuta, TEC ta shirya a cikin watanni 1 zuwa 2 amma akwai rahotanni game da yara da suka fi tsayi don farfadowa.
Jiyya
- Kulawa: Idan anemia yana da tausayi kuma yaronka yana da damuwa, babu magani zai iya zama dole. Likitan likitanka zai iya yaduwa jinin yaro ya ƙidaya lokaci har sai an warware shi.
- Corticosteroids: Wasu lokuta ana amfani da steroids kamar prednisone amma babu wani tabbacin shaida cewa wannan magani yana rage lokaci zuwa sake dawowa.
- Transfusion: Idan anemia yana da tsanani ko kuma yaronka alama ce daga anemia (rashin tsoro, gajiya, rashin ƙarfi, numfashi mai tsanani, da dai sauransu) za'a iya ba da jini jini.