Ehlers-Danlos Syndrome Overview

Sadarwar Ƙungiyar Sadarwa

Ehlers-Danlos Syndrome wata ƙungiya ce ta haɗuwa da lalacewar nama, wadda ta haifar da collagen mara kyau (wani sinadarin gina jiki a cikin haɗin haɗuwa). Nau'in haɗin gwiwar yana taimakawa wajen tallafin fata, tsokoki, ligaments, da gabobin jiki. Mutanen da suke da lahani a cikin haɗin haɗin haɗin da ke haɗuwa da Ehlers-Danlos Syndrome na iya samun alamun bayyanar da suka hada da haɗin jini na haɗin gwiwa , fata wanda aka sauƙaƙe da tayar da hankali, da kuma kyakyawa.

Akwai manyan muhimman bayanai shida na Ehlers Danlos Syndrome.

Hanyoyi shida na Ehlers-Danlos Syndrome

An adana Ehlers-Danlos Syndrome cikin nau'i shida:

Hypermobility Irin Ehlers-Danlos

Babban magungunan da ke hade da Hypermobility Type of Ehlers-Danlos Syndrome shine haɗin haɗin gwiwar haɗin kai wanda ya shafi manyan kwakwalwa. Abubuwan haɗin gwiwa da haɓakawa sune matsala mai maimaitawa. Hanyoyin fata (stretchiness, fragility, and bruising) ba su kasance ba sai dai ga maƙasudin bambancin ƙwayar cuta, a cewar Ehlers-Danlos Foundation. Jin zafi na ƙwayoyin cuta ba shi da kyau kuma yana iya zama debilitating.

Na'urar gargajiya na Ehlers-Danlos

Babban alamar da ke hade da irin na Ehlers-Danlos shine cututtuka na fata (stretchiness) na fata tare da scars, ƙididdigar hematomas, da kuma kyandun da ke dauke da mai da yawa wanda aka samo su a kan matsaloli.

Har ila yau, haɗin kai na haɗin gwiwa yana nuna bayyanar asibiti na Classical Type.

Nau'in irin na Ehlers-Danlos

Kwayar cututtuka na Ehlers-Danlos yana dauke da mafi tsanani ko mummunan yanayin Ehlers-Danlos Syndrome. Tsuntsaye ko rarraba jiki zai iya faruwa wanda zai haifar da mutuwar kwatsam. Skin yana da bakin ciki sosai (ana iya gani da sauƙi ta hanyar fata) kuma akwai nauyin gyaran ido na musamman (babban idanu, hanci mai laushi, kunnuwa ba tare da kunnuwa ba, gajere da kuma gashin gashi).

Kwancen kafa na iya zama a lokacin haihuwa. Abubuwan haɗakar haɗi ta haɗin kai kawai yana ƙunshe da lambobi.

Kyphoscoliosis Irin Ehlers-Danlos

Haɗin haɗin gwiwar da aka ƙayyade (rarrabuwa) da kuma rauni mai tsoka yana gani a haihuwa tare da Kyphoscoliosis Type Ehlers-Danlos. Ana lura da Scoliosis a lokacin haihuwa. Damarar mutum, ƙwaƙwalwa mai laushi (haddasa mummunan zuciya ko rami a cikin fata), sauƙaƙawa mai sauƙi, ƙwaƙwalwar ido (ido) da kuma rushewar kwayar cutar yiwuwar bayyanuwar asibitoci da kuma rushewa na yau da kullum.

Arthrochalasia Irin Ehlers-Danlos

Sakamakon bambancin yanayin Arthrochalasia irin na Ehlers-Danlos shine lalacewar rikici. Babban haɗin gwiwa mai haɗaka tare da sauye-sauye da sauye-sauye yana na kowa. Turawa mai tsabta, cutarwa mai laushi, lalacewar nama, fassarar ƙwayar cuta, asarar sautin tsoka, Kyphoscoliosis, da osteopenia (kasusuwa da ba su da yawa fiye da al'ada) ma yana yiwuwa bayyanuwar ta asibiti.

Dermatosparaxis Irin Ehlers-Danlos

Ƙananan launi da ƙwanƙwasawa sune halaye na Dermatosparaxis Type Of Ehlers-Danlos. Rubutun fata yana da taushi da sagging. Hernias ba sananne ba ne.

Ƙara Sanarwar Ehlers-Danlos Syndrome

Irin nau'ikan Ehlers-Danlos Syndromes suna biye da su bisa ga bayyanar ƙwaƙwalwar da ke da matsala.

Kariyar kariya, kulawa da tausayi, kariya ta hadin gwiwa, da kuma karfafa karfafawa sune muhimman al'amurran shirin shirin. Halin da ke cikin lalata da kuma wani lokacin muni yana shafi kimanin 1 cikin mutane 5,000. Akalla mutane 50,000 na Amirka suna da Ehlers-Danlos Syndrome. An kiyasta cewa kashi 90 cikin 100 na mutanen da ke fama da rashin lafiya na Ehlers-Danlos ba su da tabbas sai lokacin da ya faru na gaggawa wanda ya buƙatar gaggawa. Idan ka fuskanci duk wani bayyanar cututtukan da ke hade da EDS, tuntuɓi likitanka.

> Sources:

> Menene EDS? Ƙasar ta Ehlers-Danlos.

> Ehlers-Danlos, EWorldwire, 5/2/06