Gabatarwa ga Guillain-Barre Syndrome

Wani Ciwon Kai tsaye na Tsarin Abubuwan Hulɗa na Ƙungiyar Tsuntsauran Ƙungiya

Guillain-Barré Syndrome (Geel-on ko wani lokacin Gee-yon Barr-ay) yana nufin wani ɓangaren cuta wanda yakan haifar da rauni na tsoka, asarar rayuka, dysautonomias , ko wasu hade da uku. Ciwo na Guillain-Barré (GBS) wata cuta ce ta jiki ta jiki, wadda ke nufin cewa tsarin jiki na jikin kansa yana kai hari ga jijiyoyi a waje da ƙwaƙwalwar ƙwaƙwalwa.

Ba kowa ba ne, yana shafi guda ɗaya ko biyu ne kawai ga mutane 100,000.

Don fahimtar yadda Guillain-Barré ya lalata tsarin da ba tausayi, yana da muhimmanci mu fahimci bit game da yadda kwayoyin jikinsu ke aiki akai-akai. Jikin jikin kwayar halitta na kwance yana cikin ko kusa da ƙananan kashin. Nada yayi magana ta hanyar aika sakonni a tsawo mai tsawo, mai tsawo da ake kira axon. Wadannan ayoyin suna aika sigina daga jiki na kwayar jijiya don tsokoki don yin tsokoki da kuma aika sakonni daga masu sauraro na jiki zuwa jikin kwayar halitta domin ya ba mu damar ji.

Zai iya taimakawa wajen yin tunani akan wani abu kamar yadda waya take aikawa da lantarki zuwa ko daga sassa daban-daban na jiki. Kamar wayoyi, mafi yawan kayan aiki suna aiki mafi kyau idan ana kewaye da su.

Maimakon gyare-gyare na roba da kewayar kayan aiki na injiniyoyi, ana amfani da kayan aiki da yawa a cikin myelin. Myelin ne ya zama ta hanyar kwantar da hankalin kwayoyin da ke kewaye axon na jijiya.

Wadannan kwayoyin halitta suna karewa da kuma ciyar da kayan aiki, da kuma taimakawa gudunmawar siginar lantarki.

Ganin cewa axon wanda ba shi da karfi ya buƙaci ions su yi tafiya a ciki kuma daga cikin tsawon tsigon, magungunan da aka ƙaddamar ne kawai yana buƙatar jijiyar ta yi haka a wuraren da aka zaɓa. Wadannan mahimman suna da ake kira nodes, inda myelin ya raguwa a ciki don ya bada izinin ions.

Ainihin, maimakon tafiya cikin tsawon tsayin, sigin na lantarki yayi tsalle da sauri daga kumburi zuwa kumburi, abubuwa masu sauri tare.

Ta yaya Guillain-Barré Syndrome ke ci gaba

Guillain-Barré Syndrome yana haifar da tsarin jiki na jiki wanda ke kaiwa ga jijiyoyi na jiki. Gaskiyar cewa ciwo yakan kasance a kan bayan kamuwa da cuta (ko kuma mawuyacin hali, bayan rigakafin rigakafi) ya haifar da mu tsammanin cewa a matakin kwayoyin, wasu magunguna masu kamuwa da cuta suna kama da sassan jiki. Wannan yana haifar da tsarin rigakafi don kuskuren jijiyoyin jijiyoyi na jiki, suna tunanin cewa sassan jijiya shine kamuwa da cuta. A sakamakon haka, tsarin na rigakafi ya sake yaduwar cutar da ke kai hari ga jijiyoyi.

Ta yaya Guillain-Barré Syndrome ke shafar mutum ɗaya ya dogara da inda magungunan suke kaiwa ga jijiya. Saboda wannan dalili, Guillain-Barré mai yiwuwa shine mafi kyawun tunani a matsayin iyali na cuta, wanda zai iya haifar da matsalolin daban-daban.

Maturan ƙwararrun ƙwayoyin ƙwayoyin cuta mai ƙananan jini (AIDP) shi ne mafi yawan shafuka na Guillain-Barré, kuma abin da mafi yawan likitoci suke tunanin lokacin da ake amfani da kalmar "Guillain-Barré". A AIDP, ƙwayoyin cuta ba su kai farmaki kan kwayoyin jikinsu ba, amma a maimakon haka, lalata wasu kwayoyin goyon baya waɗanda ke kewaye da axon na jijiya.

Yawanci, wannan zai haifar da canje-canje da kuma rauni wanda zai fara a cikin yatsun kafa da yatsan hannu kuma ya shimfiɗa zuwa sama, yana damuwa a kan wani abu na kwanaki zuwa makonni. Mutane tare da Guillain-Barré na iya sha wahala daga mummunan ciwo a wuraren da suka raunana kuma baya. Kamar yawancin Guillain-Barré, bangarori biyu na jiki suna da alaƙa a AIDP.

Duk da yake AIDP shine mafi yawan mutanen Guillain-Barré, akwai wasu da yawa. Wadannan sun haɗa da wadannan.

Mota mai mahimmanci da mai hankali Axonal Neuropathy (AMSAN)

A AMSAN, magunguna suna lalata axon kai tsaye maimakon lakabi na myelin. Suna yin hakan ta hanyar kai hare-hare a inda yaduwar ta na karya don bada izinin musayar ion din da ke yada sigina na lantarki.

AMSAN na iya zama mummunan hali, tare da bayyanar cututtuka a wani lokaci yana cigaba da zuwan ƙwayar cuta a cikin kwanaki ɗaya ko biyu kawai. Bugu da ƙari, dawo da AMSAN zai ɗauki shekara ɗaya ko fiye. Maimakon sake dawowa, ba al'ada ba ne ga mutane tare da AMSAN don samun matsaloli masu dorewa, kamar damuwa ko ƙuntatawa a yatsunsu.

Mota Axonal Neuropathy Aiki (AMAN)

A AMAN, kawai jijiyoyin dake sarrafa motsi suna da tasiri, saboda haka babu wata ƙari. Mutane suna so su dawo da sauri da kuma gaba daya daga AMAN fiye da sauran siffofin Guillain-Barré.

Miller-Fisher Variant

Guillain-Barré ya fi dacewa game da lokacin da ya canza yadda muke numfasawa ko kare jirginmu. A cikin Miller-Fisher bambancin Guillain-Barré, an fara fuskantar fuska da idanu. Rashin kula da ƙwayar wugwaro zai iya ba shi yiwuwa a haɗiye ba tare da abinci ko iska ba shiga cikin huhu, kara haɗari da cututtuka na huhu da kuma tsoma baki. Duk da yake dukkanin Guillain-Barré na bukatar kulawa ta kusa don ganin ko mai yiwuwa mai haɗari ya bugu ko kuma sanya shi a kan iska mai inganci, sauyi na Miller-Fisher na bukatar kulawa sosai.

Neuropathy mai daɗaɗɗa mai kwakwalwa

Mafi yawancin irin Guillain-Barré kuma yana shafar tsarin kulawa mai kwakwalwa a wasu hanyoyi, wanda zai haifar da asarar iko na ayyuka kamar sukar, zuciya, zafin jiki, da kuma karfin jini. Ƙananan kwayoyin neuropathy ne mai mahimmanci wanda yasa motsa jiki da jin dadin jiki ya ragu, amma ayyuka masu zaman kansu sun rasa. Wannan zai iya haifar da haskakawa , ƙwaƙwalwar ƙwayar zuciya , da kuma ƙarin.

Alamar da ta fi kowa na Guillain-Barré shine raguwa mai ƙarfi wanda wani lokaci ya haɗu da hasara da kuma kulawar kwaminis. Yayinda yawancin kwayoyin neuropathies ke kara tsanantawa a kan wani al'amari na watanni zuwa shekaru, Guillain-Barré ya canza kwanaki da wasu lokuta. Saboda Guillain-Barré zai iya haifar da rauni wanda yake da tsanani sosai cewa mutum mai wahala ba zai iya yin numfashi a kansa ba, yana da muhimmanci ka samu taimako a wuri-wuri idan ka lura da wadannan bayyanar cututtuka.

Source

Yuen T. Saboda haka, Ci gaba: Kwararrun Neuropathies, Ƙananan Neuropathies, Matsalar 18, Lamba 1, Fabrairu 2012

Braunwald E, Fauci ES, et al. Ka'idodin Magungunan Hoto na Harrison. 16th ed. 2005.