Scleroderma ba cuta ce kawai ba
Scleroderma alama ce ta rukuni na cututtuka da suke da rikitarwa ta hanyar ci gaban haɗari na nama mai launi , da jiki wanda ke goyan bayan fata da gabobin ciki. Mutane da yawa masu ilimin maganin ilimin lissafi suna magana ne game da cutar kamar yadda sclerosis na jiki da kuma ƙwayar fata kamar scleroderma. Scleroderma yana nufin "fata fata," wanda aka samo daga kalmomin Helenanci sklerosis (wanda ke nufin wuya) da kuma derma (wanda ke nufin fata).
Scleroderma an dauke shi ne da cututtukan rheumatic (yanayin da ke cikin kumburi da ciwo a cikin tsokoki, kwakwalwa, ko nama mai fibrous) da kuma cututtukan nama na haɗi.
Wasu nau'o'in scleroderma suna da tsari marar iyaka wanda ke da mahimmanci da fata. Sauran iri sunfi rikitarwa, suna shafi jini da gabobin ciki kamar zuciya, huhu, da kodan.
Akwai manyan nau'o'i biyu na scleroderma: maganin scleroderma, wanda ke shafar wasu sassa na jiki kuma ya hada da scarroderma linzami da morphea, da kuma tsarin sclerosis, wanda ke shafan jikin duka.
Kammala Scleroderma
Nauyin scleroderma da ke ciki sun shafi fatar jiki da sauran kyallen takarda, kuma wani lokacin tsoka a kasa. Ƙungiyoyin ciki ba su da tasiri.
Cleroderma mai cikewa ba zai iya cigaba da cigaba da irin wannan cuta ba. Abubuwan da aka gano suna iya inganta lokaci, amma fatar jikin da ke faruwa a yayin da cutar ke aiki zai iya zama na har abada.
Yana iya zama mai tsanani da damuwa.
Akwai nau'o'i guda biyu na scleroderma: morphea da linzamin.
Morphea
Ƙunƙun fata na fata da suke ɗauka a cikin wurare masu tsaka-tsalle masu tsabta suna rarrabe irin nau'in morphea na ƙirar scleroderma. Cibiyoyin sutura suna da hauren giwa, tare da ƙananan iyakoki. Hakan zai iya faruwa akan kirji, ciki, baya, fuska, makamai, da kafafu.
Abubuwan da suka fi dacewa suna da yawa kuma suna da ƙwayar gashi. Morphea za a iya ganowa (iyakance zuwa ɗaya ko dama, wanda ya kasance daga rabin inci zuwa inci 12 a diamita) ko kuma cikakke (ƙwayoyin fata suna da wuya da kuma duhu kuma suna yadawa a kan manyan sassa na jiki). Morphea ya shafe shekaru uku zuwa biyar, amma mutane suna iya samun launin fata na fata kuma, ko da yake suna da wuya, raunin tsoka da ya rage.
Linear
Wata maɓalli guda ɗaya ko ƙuƙwalwa mai laushi, fata mai launin fata wanda yawanci yake nuna alamar nau'in ƙwayar cuta mai ƙira. Layin yawanci yana gudana wani hannu ko kafa amma zai iya sauka a goshinsa.
Tsarin Sclerosis
Tsarin sclerosis na jiki ba kawai yana rinjayar fata amma har ya shafi jini da manyan gabobin.
Cutar cutar CREST
Mutanen da ke dauke da kwayar cutar kwayar cutar sau da yawa suna da dukkanin wadannan cututtuka, da aka sani da ciwo CREST,
- Calcinosis: Koyarwar allurar alli a cikin nau'in haɗi.
- Matsayin Raynaud: Ƙananan jini na hannayen hannu ko ƙafãfun kwangila don amsawa ga sanyi ko damuwa.
- Jigilar cututtukan zubar da ciki: Ayyukan rashin lafiya na sifa suna faruwa a lokacin da tsokoki mai tsayi a cikin esophagus rasa al'amuran al'ada.
- Sclerodactyly: Cikakken fata da ƙura a kan yatsunsu ya haifar da adadi na ƙwayar sinadaran a cikin fata.
- Telangiectasias: Ƙananan yatsun ja a hannayensu da fuska suna haifar da kumburi na karamin jini.
Limited Scleroderma
Tsarin sclerosis na jiki ya kasu kashi biyu, iyakance da yadawa.
Ƙaƙwalwar ƙananan ƙwayar yawanci tana da farawa na farko kuma an ƙuntata shi zuwa wasu sassan fata, kamar yatsun hannu, hannayensu, fuska, ƙananan makamai, da kafafu.
Rayuwar na Raynaud sau da yawa ta shahararrun shekaru kafin fatawar fata ya bayyana. Wasu suna fuskantar matsalolin fatar jiki akan yawancin jikin da ke nuna kyautatawa a tsawon lokacin, suna barin fuska da hannayensu kawai tare da muni, fata mai laushi. Calcinosis da telangiectasias sukan biyo baya.
A wasu lokutan ana amfani da ƙananan ƙwayar cuta kamar cutar CREST saboda yawancin bayyanar cutar CREST a cikin wadannan marasa lafiya.
Diffuse Scleroderma
Diffuse scleroderma yawanci yana kwatsam a farkon. Skinening thickening tasowa da sauri da kuma rufe da yawa daga cikin jiki, yawanci a cikin wani daidaitaccen alamu. Babban sassan ciki zai iya lalacewa. Kwayoyin cututtuka tare da yaduwa scleroderma sun hada da:
- Haƙuri
- Rashin ci abinci ko asarar nauyi
- Haɗin haɗin gwiwa
- Haɗin gwiwa
Skin zai iya ƙarawa, ya zama mai haske, kuma yana jin dadi da damuwa. Rashin lalacewar scleroderma yayinda yake faruwa a cikin 'yan shekaru.
Bayan kimanin shekaru uku zuwa biyar, marasa lafiya suna nuna damuwa, wani lokaci lokacin da ci gaba ba ya da yawa kuma bayyanar cututtuka sun ragu-amma hankali, saurin fata zai fara sakewa. Wani lokaci wanda aka gane yana mai laushi, a lokacin da aka yi amfani da collagen kuma jikin ya rushe kansa daga haɗari.
Ƙarshen wuraren da aka girka suna da tausasawa. Wasu fata na fata suna komawa ga abin da ya fi dacewa yayin da fatar jikin wasu ya zama mai rauni kuma m. Magunguna tare da yaduwa scleroderma suna fuskantar maganganu mafi tsanani idan sun haifar da rikitarwa mai tsanani a cikin kodan, ƙwayoyin zuciya, zuciya, da magunguna.
Kasa da kashi ɗaya cikin uku na marasa lafiya da nau'i nau'i na scleroderma sukan inganta rikitarwa mai tsanani a cikin gabobin da aka ambata.
Sclerosis Sine Scleroderma
Wasu sun gane tsarin sclerosis sine scleroderma a matsayi na uku na tsarin sclerosis. Wannan nau'i na rinjayar jini da gabobin ciki, amma ba fata.
Kalma Daga
Yana da muhimmanci a fahimci irin tsarin sclerosis wanda aka gano da kai domin ya zabi mafi kyawun maganin da yake aiki a gare ka. Kodayake babu magani ga tsarin sclerosis ko scleroderma, akwai wasu samfuran da za su taimaka maka wajen sarrafa yanayinka, rage alamun bayyanar cututtuka, kuma ci gaba da rayuwa mai kyau.
> Sources:
> Scleroderma Jagora A kan Lafiya. NIAMS. http://www.niams.nih.gov/Health_Info/Scleroderma/default.asp
> Firestein GS, Kelley WN. Kelleys Textbook na Rheumatology . Philadelphia, PA: Elsevier / Saunders; 2013.