Cutar cututtuka, ganewar asali da jiyya na PSC, Ciwon ƙwayar cutar ta ciki tare da IBD
Primar sclerosing cholangitis (PSC) wani cuta ne na hanta wanda ke haifar da kumburi da kuma raguwa da bile ducts a ciki da waje na hanta. Ba shakka abin da ya sa PSC ba, ko da yake an yi la'akari da shi matsayin yanayin kai tsaye. Ba a yi la'akari da PSC ba, amma ana tunanin cewa yana da kwayoyin halitta.
Bile wajibi ne don narkewar kitsen da kuma cire kayan kwari daga hanta.
PSC yana haifar da bile ducts don ƙuntatawa daga ƙwaƙwalwa da ƙumburi, kuma bile fara tarawa cikin hanta, wanda ya lalata shi. Wannan lalacewa yana haifar da ƙaddamarwar ƙwayar cuta da cirrhosis , wanda zai hana hanta daga yin ayyukansa masu muhimmanci. Shekaru da dama na PSC zai iya haifar da ciwon ƙwayar ƙwayar bile da ake kira cholangiocarcinoma, wanda ke faruwa a cikin 10 zuwa 15% na marasa lafiya.
PSC na cigaba da sannu a hankali a mafi yawan lokuta, amma kuma yana iya zama marar tabbas kuma barazanar rayuwa. Mutane tare da PSC zasu iya samun magani don taimakawa bayyanar cututtuka kuma zasu taimaka musu suyi rayuwa mai mahimmanci.
Rikicin Mutuwa Mai Ruwa
Yawancin lokaci, mutanen da PSC ke fama da su suna tsakanin shekarun 30 da 60, tare da matsakaicin shekarun shekarun da ake ciki na 40. PSC tana nuna yawancin mutane; 60 zuwa 75% na mutanen da aka bincikar su maza ne. Gaba ɗaya, PSC wata cuta ne da ba a sani ba.
Cutar cututtuka
Wasu mutane ba su da alamun bayyanar cututtuka a ganewar asali ko ma shekaru masu yawa bayan.
Kwayoyin cututtuka sun haɗa da:
- Diarrhea (wanda ya faru daga malabsorption na mai)
- Wulo
- Fuskantuwa (daga wani kamuwa da cuta a cikin bile ducts)
- Itching wanda sau da yawa rinjayar jiki duka
- Jaundice (yellowing fata da idanu)
Ƙunƙasaddun Cututtuka
Mutane tare da PSC sun fi samun cutar ƙwaƙwalwar jini (IBD) ko osteoporosis.
PSC yana da alaka da kututture da ciwon ciki har zuwa kashi 70 cikin 100 na marasa lafiya, amma kuma yana iya haɗuwa da cutar Crohn na babban hanji, wani lokaci ana kira Crohn's colitis . Dalilin da ke tattare da ƙungiyar IBD ba'a sani ba, amma ana tsammanin shi ne sakamakon sakamako mai mahimmanci.
Sanin asali
PSC yawanci an gano shi ta hanyar hanyar da ake kira ERCP (endoscopic retrograde cholangiopancreatography) . A lokacin ERCP, likitan zai saka wani katako a cikin bakin kuma ya kewaya ta cikin bishiya da ciki zuwa garesu na itacen biliary. An saka Dye a cikin ducts domin su nuna lokacin da aka dauki rayukan x. Ana yin nazarin hasken rana don sanin ko akwai matsaloli tare da duwatsun bile.
Sakamakon ganewar asali na PSC za'a iya tabbatar da shi ta hanyar jarrabawar jini wanda aka sani da gwajin ALK (alkaline phosphatase), kodayake sakamako mai kyau zai iya nunawa wasu yanayi fiye da PSC kawai.
Kwayoyin cutar hanta yana taimakawa wajen tabbatar da ganewar asali na PSC, da kuma kula da cigaban cutar bayan ganewar asali. An yi amfani da kwayar cutar hanta a wani asibiti a wani asibiti tare da cutar ta gida . Likita na yin gwaji zai yi amfani da allura don daukar ɗan ƙaramin samfurin hanta don gwaji ta hanyar likita.
Jiyya
Babu magani wanda aka tabbatar ya zama tasiri ga magance PSC. Bincike don neman magani mai mahimmanci a halin yanzu yana gudana. Shirye-shiryen maganin kulawa kan magance cututtuka, katsewar ci gaba da cutar, da kuma kulawa don matsalolin rikice-rikice.
Ana iya kula da bayyanar cututtuka na PSC don samun sauki ga marasa lafiya. Ana iya biyan shi da Questran (cholestyramine) ko Benadryl (diphenhydramine). Domin cututtuka na iya faruwa tare da PSC, maganin rigakafi zai iya zama dole. Saboda PSC ya shafe tare da shayar mai, kari zai zama wajibi ne don biyan rashin ciwo na bitamin mai-mai narkewa A, D, E da K.
Idan lokuttuka suna faruwa a cikin bile ducts, hanya mai mahimmanci zai zama dole don budewa ko bude su. Za a iya sanya abubuwa, waɗanda ke riƙe da ɗakunan, a cikin ducts a lokacin wannan hanya.
Idan ci gaba na PSC ya kai ga rashin hanta ko halayen biliary mai ci gaba, haɗin hanta zai zama dole. Hanyoyin daji na samar da kyakkyawar rayuwa ga masu karɓa, da kuma rayuwa na kimanin kashi 75 cikin dari.
Lokacin da za a kira likita
Idan wani daga cikin wadannan alamun bayyanar ya faru da PSC, kira likitanku:
- Abun ciki na ciki
- Ƙananan duhu ko duhu
- Jaundice
- Zazzabi a kan 100.4
- Ruwa da jini
Sources :
Medicine Johns Hopkins. "Harkokin Cholangitis na Farko." Jami'ar Johns Hopkins 2013.
Karlsen TH, Hampe J, Wiencke K, Schrumpf E, Thorsby E, Lie BA, Broomé U, Schreiber S, Boberg KM. "Harkokin Halittar Halitta da ke Haɗaka da Ciwon Flammatory Ciwon Biki Ba Zai Haɗu da Haɗarin Kwayar Aiki na Sclerosing Cholangitis ba." A J Jastroenterol Jan 2007.
A Merck Manual. "Fasahar Sclerosing Cholangitis (PSC)." Merck & Co, Inc Satumba 2007.
Van Steenbergen W, De Goede E, MP na MP, Reinders J, Tilanus M, Fevery J. "Harkokin Farko na Sclerosing Cholangitis a 'Yan'uwan Biyu: Rahoton Ɗabi'a da Tabbatar da Musamman HLA da MICA Genotyping." Eur J Gastroenterol Hepatol Jul 2005.