Hirschsprung ta cutar shi ne dalilin haifuwa ta hanzari ko ɓoyewa.
Hirschsprung's Disease
Hirschsprung cutar ba abu ba ne, wanda ke faruwa a kimanin 1 cikin kowace haihuwa 5,000.
An lalacewa ta hanyar rashin yawan kwayoyin jikina (kwayoyin jikinsu) a ƙarshen haɗin da kuma dubun. Dandalin peristalsis na al'ada yana buƙatar waɗannan kwayoyin jikina, don haka ba tare da su ba, baza ka sami takunkumi irin na hanji wanda ke motsa abubuwa tare, haifar da su ya zama kwangila da kuma katange sashi daga ɗakin.
Wannan yana haifar da rikice-rikice, wanda shine alamar bayyanar wannan cuta.
Harschsprung ta cuta cututtuka
Yara jariran zasu wuce ƙwaƙwalwar ƙwayar su na farko (gishiri mai baƙar fata) a cikin sa'o'i ashirin da hudu na rayuwa.
Yawancin yara tare da cutar Hirschsprung za su yi jinkirin wucewa cikin mahaifa. Sauran wasu za su ci gaba da ƙarfafa asibiti daga baya a farkon watanni na rayuwa. Ko ta yaya, zai iya haifar da haɗari na intestinal, tare da alamu da alamun da yawa da suka haɗa da su, ciki har da:
- ƙwaƙwalwar ciki
- vomiting, wanda zai iya zama bilieux
- matalauta ciyar
- Matalauta mara kyau
Hirschsprung ta gwajin cutar
Jaraba da za a iya yi don ganewar cutar Hirschsprung ta cuta kuma ya hada da:
- radiyoyin hasken rana, wanda zai iya nuna jigilar hanzarin hanzarin hanji da rashin isasshen gas da tayi a cikin dubun
- watau barium enema, wanda zai iya nuna wani wuri mai sauyawa ko wani yanki tsakanin mazauni na al'ada da yankin da aka ƙuntata da rashin raunin ganglion
- mai jarrabawar jarrabawa, gwajin da ya dace da matsa lamba na jaririn da ke ciki wanda ya kasance a cikin dubun
Don tabbatar da ganewar asali, an yi nazarin kwayar halitta, wanda ya kamata ya nuna rashin raunin ganglion a karshen mazaunin da kuma madaidaiciya.
Jaraba don tayar da Hirschsprung ya kamata ya fara tare da barium enema.
Idan barium enema ya zama al'ada, to akwai ƙananan damar da yaron yake da Hirschsprung. Yaran da ke dauke da barium enema ko wadanda suka kasa maganin likita don magancewa ya kamata su ci gaba da samun bitar kwayoyin halitta.
Hirschsprung's Disease Treatments
Jiyya na cutar Hirschsprung shi ne ta gyare-gyare, wadda ta ƙunshi farko da ta samar da launin colostomy sannan daga bisani ya cire sashin sashin ba tare da kwayoyin jikina ba kuma ya haɗa da sassan jikin lafiya (tare da aiki).
A wasu lokuta a wani lokacin zai yiwu a yi hanya guda-ta hanyar hanya ko ma a yi aikin tiyata ba tare da laparoscopically ba.
Irin gyaran gyare-gyaren gyare-gyare zai iya dogara ne akan ƙayyadadden yanayin ɗanka. Alal misali, wasu ƙananan yara suna da rashin lafiya lokacin da aka fara bincikar su don yin aikin tiyata daya.
Abin da Kuna Bukata Ya San Game da Cutar Hirschsprung
Wasu abubuwa da za su sani game da cutar Hirschsprung sun hada da cewa:
- Har ila yau ana kiransa Megacolon na aganglionic
- ya fi kowa a cikin yara
- ana iya haɗuwa da Down syndrome , ciwon daji na Waardenburg, neurofibromatosis, da sauran ƙwayoyin cuta kuma ana tsammanin za a haifar da maye gurbi a cikin jinsin da dama
- kodayake yawanci cutar da jariran, Hirschsprung na wani lokaci ake zargi da damuwa a cikin 'ya'yan da suka tsufa tare da rikice-rikice na yau da kullum, musamman ma idan ba su da magunguna na al'ada ba tare da taimakon assassin ko maɗaukaka ba ko kuma basu ci gaba da rikicewa ba sai bayan an yaye su daga nono.
- an kira shi ne ga Harald Hirschsprung, masanin ilimin likita wanda ya bayyana yara biyu da cutar a 1887 Copenhagen
Mai ilimin likitancin yara da likitan likitancin yara zai iya taimakawa wajen bincikar cutar da kuma kula da ɗanku tare da cutar Hirschsprung.
> Sources:
Hirschsprung's Disease. Ilimin likitancin yara da cutar cututtuka (Darasi na huɗu), 2011, Shafukan 576-582.e2
Hirschsprung cuta. Harkokin Yara da Makarantar Harkokin Yara (Fita na Bakwai), 2012, Shafuka 1265-1278